Children with congenital aortic stenosis have "excessive" left ventricular hypertrophy with reduced resting systolic wall stress that allows for supernormal ejection performance. If aortic stenosis is uncorrected, this pattern persists until adulthood. The effect of removing the aortic pressure gradient on left ventricular hypertrophy and wall stress in children with congenital aortic stenosis ...

IN contrast to the usual clinical course of congenital aortic valvular stenosis in older children, the infant with severe aortic stenosis often has early symptomnatology, a malignant clinical course with severe cardiac failure, and a grim prognosis. Congenital aortic valvular stenosis inl inifancy is generally considered to occur ill two formns: (1) an isolated lesion, similar to those eases ob...

ISOLATED congenital mitral stenosis is an extremely rare condition. Only 8 cases have been reported in the literature, whereas 37 cases are recorded in association with other cardiac anomalies, such as patent ductus arteriosus, aortic stenosis, coarctation of the aorta, and aortic valve anomaly.' This paper describes 2 female infants, 4 months and 3 months old, respectively, with isolated conge...

Aortic valve stenosis is the obstruction to outflow from the left ventricle because of an abnormal aortic valve. The discharge restriction to the systemic ventricle may also be produced by an anomaly at a sub or supravalvar level. Nevertheless, the most common site of occurrence is by far the annulus (70%). Although congenital aortic stenosis is frequently associated with other significant card...

Described herein are five patients who had double left-sided cardiac valve replacement for mitral and aortic valve stenosis resulting from two different etiologies: rheumatic heart disease, the cause of the mitral stenosis, and congenital heart disease (bicuspid valve), the underlying cause of the aortic stenosis.

IN 21 INFANTS, each with symptomatic congenital aortic stenosis and left ventricular cavity of nearly normal size studied clinically,' evidence for mitral insuffiiegncy was frequently encountered. In five of the patients left ventriculography was done and, in each, mitral insufficiency was demonstrated. This background of experience led us to study, in particular, the mitral valve in specimens ...

Data from 204 children and infants who underwent aortic balloon valvuloplasty between 1982 and 1986, reported to the Valvuloplasty and Angioplasty of Congenital Anomalies Registry, were reviewed. Valvuloplasty was successful in 192 of 204 children, reducing the peak systolic left ventricular ejection gradient from 77 +/- 2 to 30 +/- 1 mm Hg, p less than 0.001. The same degree of aortic stenosis...

The objective of this study was to assess the effectiveness of balloon valvuloplasty in the young adult with congenital aortic stenosis and to compare its effectiveness with children. Percutaneous balloon valvuloplasty is effective in children with congenital aortic stenosis, but not in adults with acquired calcific aortic stenosis. Because effectiveness of balloon valvuloplasty in young adults...

This report describes 30 patients under the age of 30 years with rheumatic aortic stenosis, presenting with combined aortic and mitral stenosis. Three patients had additional tricuspid stenosis. Twenty-eight patients gave a history of rheumatic polyarthritis. The diagnosis was confirmed by right and left heart catheterisation in all. The murmur of aortic stenosis was not initially present in 8 ...