abstract hypoplastic right ventricular is a rare congenital heart disease. a few cases have been reported. we presented a case with hypoplastic right ventricular and multiple associated anomaly (ventricular septal defect, atrial septal defect and pulmonary stenosis) in whom the main concern was whether biventricular repair or fontan type surgery would be the optimal management in this patient. ...

critical pulmonary valve stenosis (cpvs) and atrial septal defect (asd) is an uncommon form of congenital heart disease. concurrent transcatheter pulmonary valvuplasty and closure of secundum atrial septal defect appears to be an interesting alternative to surgical correction. we present the simultaneous balloon valvuloplasty of critical pulmonary stenosis (ps) with supra systemic right ventric...

T HE MANAGEMENT of patients with congenital communications between the ascending aorta and the main pulmonary artery is a challenging problem, not only in the establishment of the correct diagnosis preoperatively, but in subsequent surgical treatment as well. Although often described as a rare malformation, aortopulmonary septal defect will probably be encountered in any large group of patients...

The importance of identifying this anomaly is that it is associated with other congenital malformations in over 20% of cases, most commonly being associated with cardiovascular anomalies and congenital dislocation of hip. Of the 44 infants with this syndrome, Pape and Pickering found 27 to have major anomaly of skeletal, genitourinary, respiratory and cardiovascular systems. The disorder most c...

Congenital pericardial defects are rare and asymptomatic for both partial and complete defects. However, some patients can experience syncope, arrhythmia, and chest pain. When a patient experiences a symptom, it may be caused by herniation and dynamic compression or torsion of a heart structure including the coronary arteries. Diagnosis of a congenital pericardial defect may be difficult, espec...

this study was conducted to assess the incidence of abnormalities of ventricular depolarization (late potentials) in children with sinus rhythm after open heart surgery and their relation to spontaneous ventricular tachycardia. open heart surgery, particularly operations involving ventriculotomy, may predispose patients to the development of ventricular tachycardia (vt) or ventricular fibrillat...

Admas-Oliver syndrome is a rare autosomal dominant disease of congenital development defects association with aplasia cutis. All of 81 reported cases were of 32 group families. These two cases had congenital scalp cutis aplasia with developmental defect and hypoplasia of left foot digits in case 1.Congenital deaf-mute in both can added to the past known findings in this syndrome. Thoracic defor...

Double-chambered right ventricle (DCRV) is a rare congenital heart disorder involving 2 different right ventricle (RV) pressure compartments that is often associated with ventricular septal defect (VSD). Usually, the obstruction is caused by an anomalous muscle bundle crossing the RV from the interventricular septum to the RV free wall. We are reporting a case of double-chambered right ventricl...

The present study of 47 necropsy cases of congenital heart disease has revealed that cardiac defects occur as frequently in the African as in the non-African. The types of congenital heart disease and the associated non-cardiac malformations are similar to what has been described in non-Africans. Tetrad of Fallot was the commonest type of multiple defect and ventricular septal defect the most c...