Between 1980 and 1993, 20 patients less than 1 year of age underwent operations for congenital mitral valve disease. Ten patients had congenital mitral incompetence and 10 had congenital mitral stenosis. Mean age was 6.6 +/- 3.4 months and mean weight was 5.6 +/- 1.5 kg. Atrioventricular canal defects, univentricular heart, class III/IV hypoplastic left heart syndrome, discordant atrioventricul...

The pulmonary function of ten adult patients with congenital pulmonary valvular stenosis was investigated. The patients clearly showed smaller lungs than healthy control subjects of equivalent age and height; lung elastic recoil pressure was normal at any given percentage of measured total lung capacity, indicating that postnatal parenchymal damage is not the cause of the small lungs. The lung ...

FEBRUARY 2004 I ENDOVASCULAR TODAY I 31 D uring the last 2 decades, percutaneous endovascular therapies have revolutionized the treatment of coronary artery disease. However, the development and dissemination of percutaneous approaches to heart valve disease have been less rapid. Whereas rheumatic mitral stenosis and congenital aortic stenosis are effectively managed by balloon valvuloplasty in...

A 14-year-old patient with the complex congenital heart defect of transposition of great arteries, ventricular septal defect and pulmonary stenosis, after the "réparation à l'etage ventriculaire" operation at the age of 3, was admitted to the hospital with critical pulmonary stenosis with a maximal right ventricle-pulmonary artery (RV-PA) gradient of 110 mm Hg. Transcatheter pulmonary valve imp...

The morphology of the central pulmonary artery was studied by selective angiography in 21 previously unoperated patients (aged 11 days-21 years, median 4 years) with pulmonary atresia associated with various types of congenital heart disease. Angiographic findings were confirmed at operation in 10 patients. There was juxtaductal obstruction of the left pulmonary artery in two thirds of the pati...

BACKGROUND Congenital lesions of the mitral valve are relatively rare and are associated with a wide spectrum of cardiac malformations. The surgical management of congenital mitral valve malformations has been a great challenge. OBJECTIVES The aim of this study was to evaluate the early and intermediate-term outcome of congenital mitral valve (MV) surgery in children and to identify the predi...

Combined congenital aortic and pulmonary valvular stenosis is a rare heart defect. Prevalence of severe combined valve accounts about 0.01% also has association with many syndromes. This combination presents unusual diagnostic as well management problems. Apart from few case reports, there little in the literature on both semilunar valves its management. We present this 9 year old boy which was...

Pulmonary artery aneurysm (PAA) is generally a rare lesion, and there is no definitive approach for it. We report the case of a 45-year-old man who was admitted for the evaluation of dyspnea. In childhood, he had been diagnosed with PAA with congenital pulmonary valve stenosis and regurgitation, and he had a percutaneous transvenous pulmonary valve commissurotomy. Transthoracic echocardiogram s...