Adenoid cystic carcinoma (ACC), is one of the most common primary malignant tumors of the lacrimal gland. It accounts for less than 4% of all lacrimal gland tumours. Mean age of incidence is 40 years 1 . It has a poor prognosis, in view of its locally invasive and metastatic potential .2-7 . Radical Excision with negative margin is the treatment of choice. However, the complex anatomy of orbita...

Brooke-Spiegler syndrome (BSS) is an inherited autosomal dominant disease characterized by the development of multiple adnexal cutaneous neoplasms most commonly spiradenoma, cylindroma, spiradenocylindroma, and trichoepithelioma. Multiple familial trichoepithelioma (MFT) is a phenotypic variant of the disease characterized by the development of numerous trichoepitheliomas (cribriform trichoblas...

Four cases of adenoid cystic carcinoma (cylindroma) of accessory salivary tissue are described, and the diagnostic difficulties experienced are emphasized. The tumour infiltrates cranial and other nerves and may invade the central nervous system by this route. It is highly malignant and may metastasize widely both by haematogenous and lymphatic pathways. The tumour is radiosensitive and it is s...