We describe a case of pediatric Sjögren's syndrome with progressive neurologic involvement. At age 4 years, she had been diagnosed with Melkersson-Rosenthal syndrome. After being stable with facial diplegia and swelling for 5 years, she acutely presented with diplopia, vertigo, and ataxia. Cranial magnetic resonance imaging (MRI) showed a left dorsal midbrain lesion. Serologic and histopatholog...

The first report of the congenital facial diplegia syndrome, or Moebius syndrome, was that of Graefe (1880). Moebius reported cases in 1888 and 1892 and reviewed the prior case reports, thus gaining eponymic distinction. Since that time, some authors have broadened the definition of the Moebius syndrome, as for example, Henderson (1939), who considered some cases of congenital unilateral facial...

Although traumatic injury of the facial nerve is a relatively common condition in neurosurgical practice, bilateral lesions related to fracture of temporal bones are seldom seen. We report the case of a 38-year-old patient admitted to Intensive Care Unit after severe head trauma requiring ventilatory support (Glasgow Coma Scale of 7 on admission). A computed tomography (CT) scan confirmed a lon...

A newborn male with Möbius syndrome, Poland anomaly, and dextrocardia is described. This is the second case reported of Poland-Möbius syndrome associated with dextrocardia. The patient presented with strabismus, facial diplegia, difficulty in swallowing, hypoplasia of the left pectoralis major muscle, partial absence of the upper costal cartilages, absence of the left areola, hypoplasia of the ...

CASE REPORT The patient is a 60-year-old heterosexual male with a past medical history of morbid obesity and chronic obstructive pulmonary disease. He had been in his usual state of health until approximately four weeks prior to admission, when he developed low grade fever, rhinorrhea, sore throat and diffuse arthromyalgias. Fever resolved promptly after treatment with amoxycillin and clavulani...

Thus Harlan (1881) described the appearance of a patient with bilateral congenital facial and external rectus paralysis. Chisholm's account (1882) was equally clear. The collation of cases of congenital facial palsy combined with other cranial muscle weakness by Mobius (1892) led to more general recognition of nuclear degeneration (as he termed it), or agenesis, and to eponymous fame. More rece...