The case is described of a unilateral retinoblastoma in a 7-year-old girl which was initially misdiagnosed because of massive anterior segment involvement in the apparent absence of a retinal lesion. Only on histopathological examination of the enucleated eye was the presence of retinal tumour established, this being confined to two minute foci at the extreme periphery.

The aim of the present study was to check one of the main assumptions of the interhemispheric imbalance hypothesis, namely, the prediction that the severity of neglect should be reduced by conditions activating the right hemisphere. To achieve this, a group of neglect patients was studied using a slightly modified version of the limb activation technique. The (verbal or visuo-spatial) nature of...

how to cite this article: gunawan pi, lusiana l, saharso d. hemispherectomy procedure in proteus syndrome. iran j child neurol.summer 2016; 10(3):86-90   objective proteus syndrome is a rare overgrowth disorder including bone, soft tissue, and skin. central nervous system manifestations were reported in about 40% of the patients including hemimegalencephaly and the resultant hemicranial hyperpl...

A 45-year-old woman with normal physical and mental development, who had intractable epilepsy since her childhood, had neither cognitive nor neurologic deficits. Her MRI demonstrated right hemimegalencephaly (HME) with an increase in the hemispheric volume and enlargement of the right lateral ventricle (figure 1), Figure 1 T2-weighted MRIs showing an increase in the right hemispheric volume (A)...

Hypomelanosis of Ito (HI) is a rare neurocutaneous syndrome with characteristic whirled hypopigmented skin lesions and neurological manifestations. Less consistently, there may be non-neurological manifestations that include ophthalmic, musculoskeletal, craniofacial, cardiac, genitourinary, and gastrointestinal involvements. We report a case of HI, with typical skin lesions in association with ...