نتایج جستجو برای: higashi syndrome

تعداد نتایج: 622457  

2008
H. N. Usha Preetha D. Prabhu M. Sridevi Kishore Baindur C. M. Balakrishnan

The Chediak Higashi Syndrome (CHS) is a rare autosomal recessive disease characterized by partial oculo-cutaneous albinism, frequent pyogenic infections, presence of giant granules in leucocytes and other granule containing cells(l). To date less than 150 cases have been reported in the world literature. This includes a pregnant lady who delivered a normal child(2). The first case in India was ...

Journal: :Blood 2005
Marc Tardieu Catherine Lacroix Bénédicte Neven Pierre Bordigoni Geneviève de Saint Basile Stéphane Blanche Alain Fischer

Three patients with Chediak-Higashi syndrome underwent allogeneic bone marrow transplantation between the ages of 2 years 9 months and 7 years. The outcome was uneventful, with sustained mixed chimerism. No subsequent recurrent infections or hemophagocytic syndrome were observed. At the age of 22 to 24 years, these 3 patients developed a neurologic deficit combining difficulty walking, loss of ...

Journal: :Physical review letters 1996
Susaki Sekiyama Kobayashi Mizokawa Fujimori Tsunekawa Muro Matsushita Suga Ishii Hanyu Kimura Namatame Taniguchi Miyahara Iga Kasaya Harima

T. Susaki,1 A. Sekiyama,1 K. Kobayashi,1 T. Mizokawa,1 A. Fujimori,1 M. Tsunekawa,2 T. Muro,2 T. Matsushita,2,* S. Suga,2 H. Ishii,3 T. Hanyu,3 A. Kimura,4 H. Namatame,5 M. Taniguchi,5 T. Miyahara,6 F. Iga,5 M. Kasaya,7 and H. Harima8 1Department of Physics, University of Tokyo, Bunkyo-ku, Tokyo 113, Japan 2Department of Material Physics, Osaka University, Toyonaka, Osaka 560, Japan 2Department...

Journal: :Human reproduction 2015
Kazuhiro Kawamura Yuan Cheng Ying-Pu Sun Jun Zhai Cesar Diaz-Garcia Carlos Simon Antonio Pellicer Aaron J Hsueh

Kazuhiro Kawamura1,*, Yuan Cheng1, Ying-Pu Sun2, Jun Zhai2, Cesar Diaz-Garcia3, Carlos Simon3,4, Antonio Pellicer3, and Aaron J. Hsueh4,* Department of Ob/Gyn, St. Mariana University, Kawasaki, Japan Reproductive Medical Center, The First Affiliated Hospital of Zhengzhou University, Zhengzhou, China Fundación Instituto Valenciano de Infertilidad (FIVI), ValenciaUniversity and InstitutoUniversit...

2008
Yuji Hara Michio Jimbo Hitoshi Konno Satoru Odake

We show that the deformed Virasoro algebra specializes in a certain limit to LepowskyWilson’s Z-algebra. This leads to a free field realization of the affine Lie algebra ŝl2 which respects the principal gradation. We discuss some features of this bosonization including the screening current and vertex operators. Graduate School of Arts and Sciences, The University of Tokyo, Komaba, Tokyo 153-89...

Journal: :Blood 1995
E Haddad F Le Deist S Blanche M Benkerrou P Rohrlich E Vilmer C Griscelli A Fischer

Chediak-Higashi syndrome is a rare condition characterized by susceptibility to bacterial infections, defective natural killer activity, and episodes of macrophage activation known as accelerated phases. Chemotherapy can induce transient remission of the accelerated phase, but relapses become less and less sensitive to treatment and ultimately lead to death. Allogenic bone marrow transplantatio...

Journal: :Indian Journal of Medical and Paediatric Oncology 2018

Journal: :Blood 1969
S D Douglas R S Blume S M Wolff

T HE CHEDIAK-HIGASHI SYNDROME (CR5) is characterized by large abnormal cytoplasmic organelles in cells including leukocytes which contain lysosome-like structures. This rare disease is inherited as an autosomal recessive disorder, and the clinical features include partial oculocutaneous albinism, frequent and severe pyogenic infections, and the development of a lymphoma-like ( accelerated ) pha...

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