نتایج جستجو برای: poikiloderma

تعداد نتایج: 174  

Journal: :Proceedings of the Royal Society of Medicine 1931

2014
Alexandros Katoulis Michalis Makris Stamatis Gregoriou Eustathios Rallis Antonis Kanelleas Nicolaos Stavrianeas Dimitris Rigopoulos

We report the case of a 48-year-old, Caucasian female who presented with slowly progressing asymptomatic poikilodermatous changes of the extensor aspects of the forearms. She also had typical Poikiloderma of Civatte on the V of the neck and erythemato-telangiectatic rosacea of the central face. The patient had been practicing aroma-therapy for many years. Histologic examination revealed finding...

2018
H. M. M. T. B. Herath B. S. D. P. Keragala S. P. Pahalagamage G. H. C. C. Janappriya Aruna Kulatunga C. N. Gunasekera

BACKGROUND Dermatomyositis is a humoral-mediated inflammatory myopathy with symmetrical proximal muscle weakness and dermatological manifestations such as Gottron's papules, heliotrope rash, periungual abnormalities, and flagellate erythema. Erythroderma is a severe and potentially life-threatening dermatological condition with diffuse erythema and scaling involving more than 90% of the skin su...

2014
Neelam Suman Simrat Kaur Supreet Kaur Vandana Sarangal

Kindler syndrome is a rare hereditary disorder, associated with skin fragility. The syndrome involves the skin and mucous membrane with radiological changes. The genetic defect has been identified on the short arm of chromosome 20. This report describes a 16-year-old patient with classical features like blistering and photosensitivity in childhood and the subsequent development of poikiloderma.

2016
Aude‐Annick Suter Peter Itin Karl Heinimann Munaza Ahmed Tazeen Ashraf Helen Fryssira Usha Kini Pablo Lapunzina Peter Miny Mette Sommerlund Mohnish Suri Signe Vaeth Pradeep Vasudevan Sabina Gallati

BACKGROUND Poikiloderma is defined as a chronic skin condition presenting with a combination of punctate atrophy, areas of depigmentation, hyperpigmentation and telangiectasia. In a variety of hereditary syndromes such as Rothmund-Thomson syndrome (RTS), Clericuzio-type poikiloderma with neutropenia (PN) and Dyskeratosis Congenita (DC), poikiloderma occurs as one of the main symptoms. Here, we ...

Journal: :Journal of the European Academy of Dermatology and Venereology : JEADV 2011
P Campolmi P Bonan G Cannarozzo N Bruscino M Troiano F Prignano T Lotti

BACKGROUND Intense pulsed light (IPL) treatment is one of the most effective procedures for patients with non-aesthetic vascular lesions in addition to signs of skin photoageing, and it has been reported as very successful in the treatment of telangiectasias, spider nevi, erythrosis, and above all, rosacea and poikiloderma. Its use is based on the principle of selective photothermolysis, which ...

Journal: :Journal of Korean Medical Science 2000
H. Y. Kang W. H. Kang

We report a 51-year-old Vietnam War veteran with an unusual variant of macular amyloidosis presenting as poikilodermatous skin lesions. The extensive mottled brown pigmentation was checkered with small hypopigmented or normal skin-colored spots and intermingled with telangiectasia. Skin biopsy revealed subepidermal amyloid deposits. There was no evidence of extracutaneous involvements. This cas...

2015
Sandra Mercier Sébastien Küry Emmanuelle Salort-Campana Armelle Magot Uchenna Agbim Thomas Besnard Nathalie Bodak Chantal Bou-Hanna Flora Bréhéret Perrine Brunelle Florence Caillon Brigitte Chabrol Valérie Cormier-Daire Albert David Bruno Eymard Laurence Faivre Dominique Figarella-Branger Emmanuelle Fleurence Mythily Ganapathi Romain Gherardi Alice Goldenberg Antoine Hamel Jeanine Igual Alan D. Irvine Dominique Israël-Biet Caroline Kannengiesser Christian Laboisse Cédric Le Caignec Jean-Yves Mahé Stéphanie Mallet Stuart MacGowan Maeve A. McAleer Irwin McLean Cécile Méni Arnold Munnich Jean-Marie Mussini Peter L. Nagy Jeffrey Odel Grainne M. O’Regan Yann Péréon Julie Perrier Juliette Piard Eve Puzenat Jacinda B. Sampson Frances Smith Nadem Soufir Kurenai Tanji Christel Thauvin Christina Ulane Rosemarie M. Watson Nonhlanhla P. Khumalo Bongani M. Mayosi Sébastien Barbarot Stéphane Bézieau

BACKGROUND Hereditary Fibrosing Poikiloderma (HFP) with tendon contractures, myopathy and pulmonary fibrosis (POIKTMP [MIM 615704]) is a very recently described entity of syndromic inherited poikiloderma. Previously by using whole exome sequencing in five families, we identified the causative gene, FAM111B (NM_198947.3), the function of which is still unknown. Our objective in this study was to...

Journal: :American journal of medical genetics. Part A 2003
Lisa L Wang Anu Gannavarapu Carol L Clericuzio Robert P Erickson Alan D Irvine Sharon E Plon

Poikiloderma with neutropenia (PN), previously referred to as Navajo poikiloderma (MIM #604173) is a rare, autosomal recessive disorder first described by Clericuzio et al. [1991] in the Navajo American Indian population [Erickson, 1999]. It is characterized by a distinctive poikilodermatous rash, noncyclical neutropenia, small stature, pachyonychia, and pulmonary disease (reactive airway disea...

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