The rare combination of intestinal lymphangiectasia with malrotation of the duodenum in a child of three months of life is described. Basing on the literature review only 3 similar cases were described in the world practice. The boy with protein-losing enteropathy was examined at Moscow Scientific Centre of Children's Health. The child had vomiting, diarrhea, loss in body weight, hypoproteinemi...

A 2 year and 11 month old boy presented in December 1994 with a history of recurrent episodes of generalized swelling of the body and loose stools for two years. He had been treated with plasma transfusion and antituberculous treatment in the past. He was the only child to his non-consanguineous parents. At birth, he was noticed to have facial asymmetry. He was breastfed for one year and at adm...

Primary Intestinal Lymphangiectasia (PIL) is a rare idiopathic congenital disorder characterized by impaired lymphatic drainage and protein-losing enteropathy [1,2]. PIL normally presents in childhood but can unusually present in adults [2]. We report a case of PIL diagnosed at antegrade double-balloon enteroscopy in a middle-aged man with isolated intermittent ankle edema and hypoalbuminemia.

A 68-year-old Japanese woman underwent radiotherapy for gastric lymphoma. Although lymphangiectasia was sparsely observed in the second portion of the duodenum before radiotherapy, the number of pinpoint white spots obviously increased after the treatment. Although the duodenal lymphangiectasia gradually progressed, the patient had no features of protein-losing enteropathy. This case highlights...

Abstract Background Intestinal lymphangiectasia is a rare disease. Thus, prospective studies are impossible, and therapy still controversial. Several medicines suggested for treatment but there no existing indications drug choice guidelines. We aimed to introduce the action mechanism of each overview in single-center experience review literature on second-line primary intestinal lymphangiectasi...