Isolated pulmonary artery agenesis (UPAA) diagnosed in adulthood is a rare congenital anomaly. It occurs during embryological development where there fusion failure between sixth aortic arch and truck of affected side. Here we report case an adult patient with isolated unilateral right aplasia.

Pulmonary agenesis is an uncommon anomaly that has been reported in isolation and in association with other congenital defects. Such defects include oesophageal atresia, cardiac malformation, horseshoe kidney, and anal atresia. Over a period of three years we have seen five neonates or fetuses with unilateral agenesis of the lung. All the cases had three or more anomalies seen in the VACTERL se...

INTRODUCTION Unilateral absence of the pulmonary artery (UAPA) or pulmonary artery agenesis is a rare congenital disorder presenting with a wide spectrum of symptoms. The clinical presentation is variable and many patients can be asymptomatic for many years and even throughout their lives. CASE PRESENTATION We report the case of a 53-year-old African-American woman who was diagnosed with righ...

Unilateral absence of the pulmonary artery (UAPA) or pulmonary artery agenesis is a rare congenital disorder presenting with a wide spectrum of symptoms. UAPA is usually associated with cardiac anomalies and surgically treated in childhood. We report a rare case of a 50-year-old woman who was diagnosed with left pulmonary artery agenesis without any other cardiac anomalies. Clinicians should be...

Hitherto descriptions of some 200 cases of this condition have been published. In the majority of these reports a single case has been presented in detail together with the investigations showing how the diagnosis was made. Some authors have recorded a small series of cases, and in an effort to increase the number there has often tended to be indiscriminate use of the term agenesis. As a result...

B-Excessive formations in the development of the lungs. 1-Azygos lobe 2-Supernumerary lobes a-Tracheal lobe b-The so-called lower accessory lobe c-Ectopic lung. The rarity of agenesis of the lung is attested to by the infrequency with which it has been reported in the literature. As of January 1, 1954, there were less than 150 cases reported in medical journals. In a review of 100 cases (96 fro...

In recent years the more frequent use of x-rays has revealed various congenital abnormalities of the lungs which had formerly passed undetected during life, since the clinical signs and symptoms may be minimal. An attempt is made here to elucidate the different pictures which may be seen in varying degrees of underdevelopment of the lungs. For clarity of description the following nomenclature i...