The goal of total anomalous pulmonary venous connection repair is to obtain an unobstructed communication between the pulmonary veins and the left atrium and removing intracardiac shunting. However, pulmonary venous obstruction orstenosis may be seen in 5-10% of patients, is usually evident in the first 6 months following surgery and may lead to pulmonary congestion, pulmonary arterial hyperten...

Background Total Anomalous Pulmonary Venous Connection (TAPVC) is a rare form of congenital heart disease (CHD) in which all pulmonary veins connect to the systemic veins, right atrium or the coronary sinus. Echocardiography is a good screening modality in picking up majority of these cases. Cross sectional imaging is often utilized to establish the anatomy and confirm the diagnoses. In this st...

1. Byard RW, Moore L: Total anomalous pulmonary venous drainage and sudden death in infancy. Forensic Sci Int 51:197-202, 1991 2. Frommelt PC, Stuth EAE: Transesophageal echocardiography in total anomalous pulmonary venous drainage: Hypotension caused by ompression of the pulmonary venous confluence during probe passage. J Am Soc Echocardiogr 7:652-654, 1994 3. Chang Y, Chang C, Wang M, et al: ...

We report 2 cases of transposition of the great arteries associated with anomalous pulmonary venous connection emphasizing the clinical findings, the diagnosis, and the evolution of the association. One of the patients had the anomalous pulmonary venous connection in its total infradiaphragmatic form, in the portal system, and the other patient had a partial form, in which an anomalous connecti...

Here we are reporting echocardiographic findings of 8 month child with Total Anomalous Pulmonary Venous Connection (TAPVC). All pulmonary veins are draining into a venous chamber (venous confluence) posterior to Left Atrium (LA). This chamber is draining in to persistent left superior vena cava (supradiaphragmatic type) with moderate (TR) and estimated (RV) systolic pressure was 88.2 mm of Hg s...

Visibility continues to be a major problem during repair of obstructed total anomalous pulmonary venous connection (TAPVC) resulting in frequent use of deep hypothermia and low flow bypass. Sutureless technique for primary repair of anomalous pulmonary venous connection is fast becoming popular. In this described modification of sutureless technique through the lateral approach, the left atrium...