Hydrometrocolpos is an uncommon congenital disorder consisting of cystic dilatation the vagina and uterus, usually caused by distal obstruction. Many urogenital malformations, ranging from persistent sinus to cloacal dysgenesis, may cause hydrometrocolpos. In obstructive, uterovaginal causes such as imperforate hymen, transverse vaginal septum are common etiologies. Early diagnosis in antenatal...

Background: Amenorrhea is defined as the absence of menarche in females reproductive age. Primary amenorrhea failure to reach by age 13 with no secondary sexual characteristics if has not occurred five years after initial breast development or patient 15 older. A transverse vaginal septum a rare congenital abnormality Mullerian duct that can cause primary amenorrhea. Transverse incidence ranges...

McKusick-Kaufman syndrome (MKS) is an autosomal recessive multiple malformation syndrome characterized by hydrometrocolpos (HMC) and postaxial polydactyly (PAP). We report a case of a female child with MKS who was transferred to the neonatal intensive care unit of Seoul National University Children's Hospital on her 15th day of life for further evaluation and management of an abdominal cystic m...

BACKGROUND Hydrometrocolpos (HMC) develops as a result of vaginal outflow obstruction and the accumulation of secretions. It might be secondary to persistent cloaca, urogenital sinus, some syndromes, presence of the vaginal septum, vaginal atresia, and imperforate hymen. Each of them has different treatment options and follow-up protocols. This study was performed to identify the etiology and t...