نتایج جستجو برای: alpha 1 antitrypsin a1at

تعداد نتایج: 2882257  

Journal: :The European respiratory journal 2013
Nicola J Sinden Robert A Stockley

Chronic obstructive pulmonary disease (COPD) is associated with tissue damage believed to result from an imbalance between serine proteinases and their inhibitors. Although the role of neutrophil elastase (NE) has been studied, it is likely that other proteinases play a role. The importance of proteinase 3 (PR3) has not been established, as specific substrates have only recently been available....

ژورنال: :iranian red crescent medical journal 0
bita geramizadeh department of pathology, transplant research center, shiraz university of medical sciences, shiraz, ir iran; transplant research center, shiraz university of medical sciences, shiraz, ir iran; department of pathology, transplant research center, shiraz university of medical sciences, shiraz, ir iran. tel: +98-7116474331, fax: +98-7116474331 zahra jowkar department of pathology, transplant research center, shiraz university of medical sciences, shiraz, ir iran leila karami department of pathology, transplant research center, shiraz university of medical sciences, shiraz, ir iran masoum masoumpour department of internal medicine, shiraz university of medical sciences, shiraz, ir iran samrad mehrabi department of internal medicine, shiraz university of medical sciences, shiraz, ir iran mohammad-ali ghayoumi department of internal medicine, shiraz university of medical sciences, shiraz, ir iran

background alpha-1 antitrypsin deficiency is a genetic disease which affects both lung and liver. this disease is a recognized factor for chronic obstructive pulmonary disease (copd). however its importance as the cause of copd in a country such as iran is unclear. objectives this study was conducted to find out the role of α-1 antitrypsin deficiency as a cause of copd in iranian patients. mate...

2017
Camille de Seynes C. Ged H. de Verneuil N. Chollet M. Balduyck C. Raherison

Alpha-1-antitrypsin deficiency (A1ATD) is a genetic condition caused by SERPINA1 mutations, which results into decreased protease inhibitor activity in the serum and predisposes to emphysema and/or to liver disease due to accumulation of the abnormal protein in the hepatic cells. In most cases the clinical manifestations of A1ATD are associated with PIZZ (p.Glu366Lys; p.Glu366Lys (p.Glu342Lys; ...

Journal: :American journal of physiology. Lung cellular and molecular physiology 2015
Angelia D Lockett Daniela N Petrusca Matthew J Justice Christophe Poirier Karina A Serban Natalia I Rush Malgorzata Kamocka Dan Predescu Sanda Predescu Irina Petrache

In addition to exerting a potent anti-elastase function, α-1 antitrypsin (A1AT) maintains the structural integrity of the lung by inhibiting endothelial inflammation and apoptosis. A main serpin secreted in circulation by hepatocytes, A1AT requires uptake by the endothelium to achieve vasculoprotective effects. This active uptake mechanism, which is inhibited by cigarette smoking (CS), involves...

2015
Ilaria Ferrarotti Beata Poplawska-Wisniewska Maria Teresa Trevisan Janine Koepke Marc Dresel Rembert Koczulla Stefania Ottaviani Raffaele Baldo Marina Gorrini Giorgia Sala Luana Cavallon Tobias Welte Joanna Chorostowska-Wynimko Maurizio Luisetti Sabina Janciauskiene Pavel Strnad

The Z deficiency in α1-antitrypsin (A1ATD) is an under-recognized condition. Alpha1-antitrypsin (A1AT) is the main protein in the α1-globulin fraction of serum protein electrophoresis (SPE); however, evaluation of the α1-globulin protein fraction has received very little attention. Serum Z-type A1AT manifests in polymeric forms, but their interference with quantitative immunoassays has not been...

Journal: :American journal of physiology. Gastrointestinal and liver physiology 2016
Youcai Tang Peter Fickert Michael Trauner Nancy Marcus Keith Blomenkamp Jeffrey Teckman

The bile acid nor-ursodeoxycholic acid (norUDCA) has many biological actions, including antiapoptotic effects. Homozygous PIZZ α-1-antitrypsin (A1AT)-deficient humans are known to be at risk for liver disease, cirrhosis, and liver cancer as a result of the accumulation of the toxic, A1AT mutant Z protein within hepatocytes. This accumulation triggers cell death in the hepatocytes with the large...

2011
Na Yang Shun Feng Kerby Shedden Xiaolei Xie Yashu Liu Charles J. Rosser David M. Lubman Steven Goodison

Background: Cancers of the urinary bladder are the fifth most commonly diagnosed malignancy in the United States. Early clinical diagnosis of bladder cancer remains amajor challenge, and the development of noninvasivemethods for detection and surveillance is desirable for both patients and health care providers. Approach: To identify urinary proteins with potential clinical utility, we enriched...

Journal: :Clinical cancer research : an official journal of the American Association for Cancer Research 2011
Na Yang Shun Feng Kerby Shedden Xiaolei Xie Yashu Liu Charles J Rosser David M Lubman Steven Goodison

BACKGROUND Cancers of the urinary bladder are the fifth most commonly diagnosed malignancy in the United States. Early clinical diagnosis of bladder cancer remains a major challenge, and the development of noninvasive methods for detection and surveillance is desirable for both patients and health care providers. APPROACH To identify urinary proteins with potential clinical utility, we enrich...

2016
Reena Berman Di Jiang Qun Wu Hong Wei Chu

Human rhinovirus (HRV) infections target airway epithelium and are the leading cause of acute exacerbations of COPD. Cigarette smoke (CS) increases the severity of viral infections, but there is no effective therapy for HRV infection. We determined whether α1-antitrypsin (A1AT) reduces HRV-16 infection in CS-exposed primary human airway epithelial cells. Brushed bronchial epithelial cells from ...

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