Primary isolated chylopericardium is a rare entity. Its exact pathophysiology is still unknown. A case of chronic isolated primary pericardium diagnosed 12 years after the initial diagnosis of an asymptomatic pericardial effusion is reported. The diagnosis was established incidentally during surgery for resection of a papillary fibroelastoma of the aortic valve.

Persistent pericardial effusion in the absence of obvious preceding or concurrent disease presents a baffling problem. In such cases chylopericardium, cholesterol pericarditis, lupus erythematosus, malignant disease, myxedema, severe anemia, and scleroderma, must be considered. Six cases are reported with large effusions present for from 1 to 11 years. The diagnostic measures to be used, the re...

1. Kobayashi Y, Amaro M, Fitzgerald PJ. Acute coronary closure after stenting: a lesson from intravascular ultrasound. Int J Cardiovasc Intervent. 1999;2:51-4. 2. Murasato Y, Suzuka H, Suzuki Y. Incomplete stent apposition in a left main bifurcated lesion after kissing stent implantation. J Invasive Cardiol. 2006;18:E279-84. 3. Costa RA, Mintz GS, Carlier SG, Lansky AJ, Moussa I, Fujii K, et al...

Pulmonary lymphangiomatosis is a rare clinical and pathological entity which is distinct from lymphangiomyomatosis and from pulmonary lymphangiectasis. We report a case of a 20 year old man with diffuse lymphangiomatosis involving the mediastinum, lungs and retroperitoneum. The patient's intrathoracic lymphangiomatosis produced restrictive and obstructive impairment of his pulmonary function, b...