OBJECTIVES/HYPOTHESIS To propose an evidence-based strategy for the management of patients with advanced otosclerosis accompanied by severe to profound hearing loss. STUDY DESIGN Systematic review of the literature and development of treatment guidelines. METHODS A systematic review was conducted on (advanced) otosclerosis and cochlear implantation or stapedotomy. We focused on hearing resu...

fact, approximately 17% (36 million) of American adults report some degree of it. Moderate to severe hearing loss can be treated with a hearing aid. Beyond a certain level of hearing loss, a conventional hearing aid no longer provides a solution. For these cases, a hearing implant such as a bone conduction implant or a cochlear implant may be a solution. Cochlear Ltd., headquartered in Australi...

OBJECTIVE Cochlear implantation is the most important treatment currently available for profound sensorineural hearing loss. The aim of this study was to investigate the etiology of hearing loss in patients with cochlear implantation, and to compare outcomes. METHODS Japanese hearing loss patients who received cochlear implants (CIs) or electric acoustic stimulation (EAS) in Shinshu Universit...

Hearing loss is one of the commonest congenital anomalies to affect children world-over. The incidence of congenital hearing loss is more pronounced in developing countries like the Indian sub-continent, especially with the problems of consanguinity. Hearing loss is a double tragedy, as it leads to not only deafness but also language deprivation. However, hearing loss is the only truly remediab...

Recent developments in the field of psychoacoustics are presented, focusing on areas which have application in the diagnosis and understanding of impaired hearing. Cochlear hearing loss often results in a loss of the compressive non-linearity that operates in normal ears; this loss is probably the main cause of loudness recruitment. Forward masking can be used as a tool to assess the strength o...

The classic view of sensorineural hearing loss (SNHL) is that the "primary" targets are hair cells, and that cochlear-nerve loss is "secondary" to hair cell degeneration. Our recent work in mouse and guinea pig has challenged that view. In noise-induced hearing loss, exposures causing only reversible threshold shifts (and no hair cell loss) nevertheless cause permanent loss of >50% of cochlear-...

Cochlear implantation in children with an asymmetrical hearing loss is now becoming more recognized as an appropriate and beneficial treatment option. In our programme, we have been implanting children with asymmetrical hearing loss since 2008. Asymmetrical hearing loss is defined as hearing loss when one ear meets criteria for cochlear implantation and the other ear has better hearing and rece...

The preservation of residual haring has emerged as an issue of concern in cochlear implantation. The indications of cochlear implantation have broadened from bilateral profound sensory neural hearing loss with normal auditory nerve function to include cases with residual hearing [1]. More emphasis is being given to the study of factors and techniques of preservation of residual hearing in order...

OBJECTIVE To evaluate magnetic resonance imaging (MRI) scans for enhancement of inner ear structures of patients with sensorineural hearing loss and documented antibodies to the 68-kd inner ear antigen. STUDY DESIGN Retrospective case review with reexamination of MRI scans. SETTING Outpatient office. PATIENTS Thirty-five patients with autoimmune sensorineural hearing loss defined by audio...

Copyright © 2007 Massachusetts Medical Society. A 4-month-old baby girl whose parents and 6-year-old brother have severe-to-profound sensorineural hearing loss is referred for consideration for cochlear implantation. Each of the baby’s parents had previously received a cochlear implant in adulthood, and her older brother had received a cochlear implant at 18 months of age. The family uses oral ...