BackgroundBronchiectasis is defined by permanent and abnormal widening of the bronchi. Although this process occurs in the context of chronic airway infection and inflammation, since there is no accurate estimation of the etiology of the disease. This study aimed to determine the most important cause of bronchiectasis in Tehran, Iran.Materials and MethodsIn this retrospective cohort study we us...

backgroundbronchiectasis is defined by permanent and abnormal widening of the bronchi. although this process occurs in the context of chronic airway infection and inflammation, since there is no accurate estimation of the etiology of the disease. this study aimed to determine the most important cause of bronchiectasis in tehran, iran.materials and methodsin this retrospective cohort study we us...

cystic fibrosis (cf) is the most common inherited disorder in caucasian populations, with over 1400 cystic fibrosis transmembrane conductance regulator (cftr) mutations. the type of mutations and their distributions varies widely between different countries and/or ethnic groups. seventy iranian cystic fibrosis patients were screened for the cftr gene mutation using arms/pcr (amplification refra...

objective(s) pseudomonas aeruginosa is the most important cause of chronic lung infections and death in patients with cystic fibrosis. determining the distribution of specific strains within patient populations is important in order to examine the epidemiology of the disease and the possibility of cross infection among patients. materials and methods forty six iranian patients with cystic fibro...

cystic fibrosis (cf) is a life-limiting autosomal recessive disorder affecting principally respiratory and digestive system . it is caused by cystic fibrosis transmembrane conductance regulator (cftr) gene mutation. the aim of this study was to determine the extent of repeat numbers and the degree of heterozygosity for c.3499+200ta(7_56) and d7s523 located in intron 17b and 1 cm proximal to the...

background: due to the predisposing conditions in patients with cystic fibrosis (cf) caused by defective mucociliary clearance facilitating colonization and invasion with candida species has dramatically increased. traditional methods for identifying problems are imminent and time-consuming. therefore, molecular techniques utilizing amplification of target dna provide quick and precise methods ...

Introduction: Patients with Cystic Fibrosis have increased risk of malnutrition. Early detection of nutritional deterioration enables prompt intervention and correction. The aims of this project were to: - Define the nutritional status of CF patients in Iran and New Zealand -    Compare and contrast the MacDonald Nutritional Screening tool  with the Australasian guidelines for Nutrition in Cyst...

BACKGROUND Antenatal screening for cystic fibrosis has been endorsed by the US National Institutes of Health. Edinburgh is the only city in the UK with an established routine antenatal screening programme for cystic fibrosis. AIMS To report the change in numbers of infants diagnosed with cystic fibrosis born in Edinburgh after the introduction of antenatal screening for the disease. POPULAT...

Cystic fibrosis in earlier days was described as “Cystic fibrosis of Pancreas” in a child. The word cystic fibrosis was coined due to the characteristic cysts and fibrosis found in the pancreas. It was a leading cause of mortality in the people of northern Europe in the 16th century. In the early years of cystic fibrosis, it was known that if the fingers of the child tasted salty after rubbing ...