A 14-year-old boy presented with several months of increasing abdominal girth and fatigue. Imaging confirmed massive ascites and hepatic congestion secondary to central hepatic venous obstruction. Several large intrahepatic collateral veins were seen draining via caudate and emissary veins. After an unsuccessful attempt at retrograde recanalization utilizing intravascular ultrasound, the right ...

Focal nodular hyperplasia and nodular regenerative hyperplasia are occasionally seen in patients with hepatic venous outflow obstruction as a consequence of circulatory stress in the liver. In addition, neoplastic processes such as hepatic adenoma, hepatocellular carcinoma, and metastatic disease may arise in these patients. Histologic evaluation is necessary when imaging modalities are unable ...

background: â budd-chiari syndrome (bcs) is a rare syndrome caused by hepatic venous outflow obstruction. the etiology of bcs differs between western and eastern countries. this article is a review of all published articles in iranian and international journals regarding different aspects of bcs (prevalence, etiology, and conventional treatments) in iran. materials and methods : â  in this revi...

Most hepatic arteriovenous shunts (HAVS) associated with hepatocellular carcinoma (HCC) occur with advanced stage liver cancer, and these patients typically have a dismal prognosis. Transcatheter arterial embolization (TAE) in this population carries significant risk. Therefore, proper patient selection is critical to determine which patients may benefit from TAE. The Child-Pugh score should be...

Hepatic outflow obstruction created by balloon occlusion of the hepatic vein induces characteristic angiographic findings in the occluded area: prolonged enhancement on hepatogram followed by reversed portal opacification on the hepatic arteriogram and perfusion defect on the arterial portogram. The following induced hepatic hemodynamic changes are suggested: hepatic arterial flow increases, an...

BACKGROUND Factor V Leiden (FVL) and prothrombin gene (G20210A) mutations are known to be associated with venous thromboembolism. Several studies have shown an association of these mutations with hepatic venous outflow tract obstruction (HVOTO). We studied the prevalence of these mutations among patients with HVOTO in northern India in comparison with healthy population. METHODS Genomic DNA f...

Background: Subacute hepatic failure (SAHF) is a complication of acute hepatitis (AH) characterized by progressive jaundice and development of ascites within 24 weeks of the onset of icterus. Its pathogenesis is unknown and its treatment is unsatisfactory. This study highlights on the possible pathogenesis of the disease. Materials and methods: Thirty-two with SAHF among 798 patients of AH who ...

A 51-year-old male firefighter with a remote history of deep vein thrombosis following ankle fracture was hospitalized at our center for a 2 week history of jaundice, ascites and right upper quadrant abdominal pain. His bloodwork on admission was significant for ALT and AST 100 times the upper limit of normal, bilirubin 30 mg/dL (normal 322), hemoglobin 16.8 mg/dL (normal 13.5-16), platelets 57...

Portal hypertensive biliopathy (PHB) is defined as biliary abnormalities associated with portal hypertension, particularly caused by extra hepatic portal venous obstruction. Clinical spectrum ranges from no symptoms to biliary obstruction and life threatening cholangitis. PHB is an unusual cause of hemobilia. We present three cases of PHB presented to us with varied clinical features and manage...

A 27-years-old female with history of venous thromboembolism secondary to Lupus anticoagulant presented with sudden onset of chest pain and dyspnea. A CT angiogram of the chest showed superior vena caval (SVC) obstruction with anterior chest wall venous collaterals and hepatic portal vein gas (HPVG), which resolved without intervention on a repeated CT-scan of the abdomen. Previously, HPVG was ...