نتایج جستجو برای: hereditary spastic paraplegia

تعداد نتایج: 94252  

2016
Eleanna Kara Arianna Tucci Claudia Manzoni David S. Lynch Marilena Elpidorou Conceicao Bettencourt Viorica Chelban Andreea Manole Sherifa A. Hamed Nourelhoda A. Haridy Monica Federoff Elisavet Preza Deborah Hughes Alan Pittman Zane Jaunmuktane Sebastian Brandner Georgia Xiromerisiou Sarah Wiethoff Lucia Schottlaender Christos Proukakis Huw Morris Tom Warner Kailash P. Bhatia L.V. Prasad Korlipara Andrew B. Singleton John Hardy Nicholas W. Wood Patrick A. Lewis Henry Houlden

The hereditary spastic paraplegias are a heterogeneous group of degenerative disorders that are clinically classified as either pure with predominant lower limb spasticity, or complex where spastic paraplegia is complicated with additional neurological features, and are inherited in autosomal dominant, autosomal recessive or X-linked patterns. Genetic defects have been identified in over 40 dif...

Journal: :genetics in the 3rd millennium 0
parva namiranian mehrvash shams joseph gleeson hossein najmabadi ariana kariminejad

spastic paraplegia 18 is an autosomal recessive disorder characterized by motor dysfunction, joint contracture and mental retardation. we describe two families as three cases. case 1 is a 35-year-old woman with and spasticity and mild weakness in lower limbs. case 2 and 3 are a sister and brother aged six and two respectively. the older sister suffered from lower limb spasticity, equinovarus an...

2012
Yu Gao Lumei Chi Yinshi Jin Guangxian Nan

PCR amplification and sequencing of whole blood DNA from an individual with hereditary spastic paraplegia, as well as family members, revealed a fragment of proteolipid protein 1 (PLP1) gene exon 1, which excluded the possibility of isomer 1 expression for this family. The fragment sequence of exon 3 and exon 5 was consistent with the proteolipid protein 1 sequence at NCBI. In the proband sampl...

Journal: :Journal of medical genetics 1995
G Woods G Black G Norbury

We report a family with an undiagnosed X linked condition. The grandmother, two of her three daughters, and one of her grand-daughters have a slowly progressive proximal weakness, brisk reflexes, poor bladder function, static reduced night vision, and IgG2 deficiency. The diagnosis of the three living symptomatic females was "hereditary spastic paraplegia plus". They have lost five male childre...

Journal: :Journal of neurology, neurosurgery, and psychiatry 1991
W Schady J P Dick A Sheard S Crampton

Central motor conduction (CMC) studies were carried out in 25 patients with hereditary spastic paraplegia (HSP). Responses evoked in the lower limbs by transcranial magnetic stimulation of the motor cortex were bilaterally absent in 33% of the patients and, when recordable, were delayed in 75% of cases. Responses in the upper limbs were mostly normal except for those from the five members of on...

Journal: :Turkiye Klinikleri Journal of Neurology 2018

Journal: :Arquivos De Neuro-psiquiatria 2023

Case presentation: Girl, 5 years old, she had not gestational and neonatal complications her parents is consanguineous. She neuropsychomotor developmental delay (NDD) dysphagia for solids at 6 months. At 2 cognitive impairment, motor with axial ataxia, appendicular hypotonia dysmetria. Her symptoms progressively worsening associated pyramidal signs. Cerebellar atrophy increased arachnoid space ...

نمودار تعداد نتایج جستجو در هر سال

با کلیک روی نمودار نتایج را به سال انتشار فیلتر کنید