نتایج جستجو برای: homozygosity mapping

تعداد نتایج: 200921  

Journal: :Journal of medical genetics 2003
L Faivre M Le Merrer L I Al-Gazali M G E M Ausems P Bitoun D Bacq P Maroteaux A Munnich V Cormier-Daire

Desbuquois dysplasia is a rare autosomal recessive chondrodysplasia characterised by short stature, joint laxity, facial dysmorphism, a "Swedish key" appearance of the proximal femur, advanced carpal and tarsal bone age, and hand anomalies consisting of phalangeal dislocations and an extra ossification centre distal to the second metacarpal. However, the latter changes are not consistently obse...

2011
Anna M. Siemiatkowska Kentar Arimadyo Luminita M. Moruz Galuh D.N. Astuti Marta de Castro-Miro Marijke N. Zonneveld Tim M. Strom Ilse J. de Wijs Lies H. Hoefsloot Sultana M.H. Faradz Frans P.M. Cremers Anneke I. den Hollander Rob W.J. Collin

PURPOSE Retinitis pigmentosa (RP) is a clinically and genetically heterogeneous retinal disorder. Despite tremendous knowledge about the genes involved in RP, little is known about the genetic causes of RP in Indonesia. Here, we aim to identify the molecular genetic causes underlying RP in a small cohort of Indonesian patients, using genome-wide homozygosity mapping. METHODS DNA samples from ...

Journal: :iranian journal of child neurology 0
joseph g. gleeson

abstract objective the last two decades have seen major advancements in our understanding of some of the most common neurodevelopmental disorders in the field of child neurology. however, in the majority of individual patients, it is still not possible to arrive at a molecular diagnosis, due in part to lack of knowledge of molecular causes of these tremendously complex conditions. common geneti...

Journal: :American journal of human genetics 2002
Mark Abney Carole Ober Mary Sara McPeek

We present methods for linkage and association mapping of quantitative traits for a founder population with a large, known genealogy. We detect linkage to quantitative-trait loci (QTLs) through a multipoint homozygosity-mapping method. We propose two association methods, one of which is single point and uses a general two-allele model and the other of which is multipoint and uses homozygosity b...

2013
Li Zhang Mohammed S. Orloff Sean Reber Shengchao Li Ye Zhao Charis Eng

Identification of disease variants via homozygosity mapping and investigation of the effects of genome-wide homozygosity regions on traits of biomedical importance have been widely applied recently. Nonetheless, the existing methods and algorithms to identify long tracts of homozygosity (TOH) are not able to provide efficient and rigorous regions for further downstream association investigation...

Journal: :Journal of medical genetics 2004
C Lagier-Tourenne E Boltshauser N Breivik M Gribaa C Bétard C Barbot M Koenig

BACKGROUND Joubert syndrome (JS) is a recessively inherited disorder characterised by hypotonia at birth and developmental delay, followed by truncal ataxia and cognitive impairment, characteristic neuroimaging findings (cerebellar vermis hypoplasia, "molar tooth sign") and suggestive facial features. JS is clinically heterogeneous with some patients presenting with breathing abnormalities in t...

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