نتایج جستجو برای: progeroid appearance

تعداد نتایج: 87138  

Journal: :Nippon Ronen Igakkai Zasshi. Japanese Journal of Geriatrics 1988

2017
Zhongxi Yang Heechul Jun Chan‐II Choi Ki Hyun Yoo Chang Hoon Cho Syed Mohammed Qasim Hussaini Ambrosia J. Simmons Seonhee Kim Jan M. van Deursen Darren J. Baker Mi‐Hyeon Jang

Aging causes significant declines in adult hippocampal neurogenesis and leads to cognitive disability. Emerging evidence demonstrates that decline in the mitotic checkpoint kinase BubR1 level occurs with natural aging and induces progeroid features in both mice and children with mosaic variegated aneuploidy syndrome. Whether BubR1 contributes to age-related deficits in hippocampal neurogenesis ...

Journal: :The Korean Journal of Internal Medicine 2009
Yun Jeong Doh Hee Kyoung Kim Eui Dal Jung Seung Hee Choi Jung Guk Kim Bo Wan Kim In Kyu Lee

Hutchinson-Gilford progeria syndrome (HGPS) and Werner's syndrome are representative types of progeroid syndrome. LMNA (Lamin A/C) gene mutation with atypical Werner's syndrome have recently been reported. Atypical Werner's syndrome with the severe metabolic complications, the extent of the lipodystrophy is associated with A133L mutation in the LMNA gene and these patients present with phenotyp...

Journal: :Stem cells 2017
Panagiotis Mistriotis Vivek K Bajpai Xiaoyan Wang Na Rong Aref Shahini Mohammadnabi Asmani Mao-Shih Liang Jianmin Wang Pedro Lei Song Liu Ruogang Zhao Stelios T Andreadis

Cellular senescence as a result of organismal aging or progeroid diseases leads to stem cell pool exhaustion hindering tissue regeneration and contributing to the progression of age related disorders. Here we discovered that ectopic expression of the pluripotent factor NANOG in senescent or progeroid myogenic progenitors reversed cellular aging and restored completely the ability to generate co...

2014
Vittoria Cenni Cristina Capanni Elisabetta Mattioli Marta Columbaro Manfred Wehnert Michela Ortolani Milena Fini Giuseppe Novelli Jessika Bertacchini Nadir M. Maraldi Sandra Marmiroli Maria Rosaria D'Apice Sabino Prencipe Stefano Squarzoni Giovanna Lattanzi

Lamin A is a key component of the nuclear lamina produced through post-translational processing of its precursor known as prelamin A.LMNA mutations leading to farnesylated prelamin A accumulation are known to cause lipodystrophy, progeroid and developmental diseases, including Mandibuloacral dysplasia, a mild progeroid syndrome with partial lipodystrophy and altered bone turnover. Thus, degrada...

2013
Fabio Coppedè

Hutchinson-Gilford Progeria Syndrome and Werner syndrome, also known as childhood- and adulthood-progeria, respectively, represent two of the best characterized human progeroid diseases with clinical features mimicking physiological aging at an early age. The discovery of their genetic basis has led to the identification of several gene mutations leading to a spectrum of progeroid phenotypes ra...

A.R Fekri M Hayatbakhsh-Abasi S Shamsodini

premature aging of Wiedmann rautenstrauch type is a rare syndrome,of which only nine cases has been reported up to 1994.this syndrome is characterized by cardiac, mental and physical problems such as skull and vertebral malformation which can be diagnosed from birth.in this article a 24 year old woman is reportef who was reffered to interal medicine clinic with the chief complaint of palpitatio...

A female one month old with features supporting a diagnosis of neonatal progeroid syndrome(WRS)  presented to our neonatology section of GB pant children hospital Srinagar .she had prenatal and post natal growth failure, generalized lipotrophy, triangular face, psedohydrocephalous, sparse scalp hair and eye brows, prominent scalp veins and greatly widened anterior fontenella.

Journal: :Proceedings of the National Academy of Sciences 1973

Journal: :Genetics 2013
Jeffrey D Stumpf William C Copeland

The importance of mitochondrial DNA (mtDNA) deletions in the progeroid phenotype of exonuclease-deficient DNA polymerase γ mice has been intensely debated. We show that disruption of Mip1 exonuclease activity increases mtDNA deletions 160-fold, whereas disease-associated polymerase variants were mostly unaffected, suggesting that exonuclease activity is vital to avoid deletions during mtDNA rep...

نمودار تعداد نتایج جستجو در هر سال

با کلیک روی نمودار نتایج را به سال انتشار فیلتر کنید