نتایج جستجو برای: propionic acidemia

تعداد نتایج: 4552  

Journal: :Biochimica et Biophysica Acta (BBA) - Molecular Basis of Disease 2002

Journal: :Clinical chemistry 1978
R E Hillman

A semimicro method for measuring propionic and other short-chain fatty acids in serum is presented. The procedure requires as little as 200 microliter of serum. Data are provided for premature infants, children, adults, and patients with propionicacidemia.

Journal: :iranian journal of child neurology 0
shadab salehpour assistant professor of pediatric endocrinology and fellowship of bone and inherited metabolic disorders, shahid beheshti university of medical sciences, tehan, iran

a clinical presentation of a metabolic disorder, often first seen in infants who present with poor feeding, vomiting, tachypnea, acidosis, hyperammonemia, ketosis, ketonuria, irritability, and convulsions or hypotonia and lethargy, findings that are otherwise suggestive of neonatal sepsis diseases with oa isovaleric and propionic acidemias, maple syrup urine disease, medium chain acyl dehydroge...

Journal: :iranian journal of allergy, asthma and immunology 0
faegheh alizadeh najjarbashi mofid children hospital, school of medicine, shahid beheshti university of medical sciences, tehran, iran mehrnaz mesdaghi department of immunology, mofid children hospital, school of medicine, shahid beheshti university of medical sciences, tehran, iran and pediatric infections research center, mofid children hospital, shahid beheshti university of medical sciences, tehran, iran mohammadreza alaei department of endocrinology and metabolism, mofid children hospital, school of medicine, shahid beheshti university of medical sciences, tehran, iran marjan shakiba department of endocrinology and metabolism, mofid children hospital, school of medicine, shahid beheshti university of medical sciences, tehran, iran aliakbar jami department of pediatric cardiology, school of medicine, army university, tehran, iran farah ghadimi department of immunology, mofid children hospital, school of medicine, shahid beheshti university of medical sciences, tehran, iran

patients with organic acidemia are prone to different infections, which lead to acidosis episodes. some studies have evaluated the status of immune system in acidotic phase in these patients, but to the best of our knowledge no study has evaluated the immune system in non-acidotic phase of the disease. in this study, thirty-one patients with organic acidemia were enrolled. for evaluation of hum...

Journal: :Molecules 2004
Jack G Parsons Danuta Stachurska-Buczek Neil Choi Peter G Griffiths Daniel A Huggins Beata M Krywult Sharon T Marino Thao Nguyen Craig S Sheehan Ian W James Andrew M Bray Jonathan M White Rustum S Boyce

The synthesis of (2S)-2-benzyloxymethyl-3-(2-fluoro-4-methoxyphenyl)- propionic acid, (2S)-2-benzyloxymethyl-3-(2-fluoro-4-methylphenyl)propionic acid and (2S)-2-benzyl-oxymethyl-3-(2,4-dimethylphenyl)propionic acid has been achieved by TiCl4 mediated alkylation of the corresponding (4R)-4-benzyl-3-[3-(2-fluoro-4-methoxyphenyl-, 2-fluoro-4-methylphenyl-, 2,4- dimethylphenyl-)propionyl]-2-oxazol...

Journal: :Journal of Dr. Behcet Uz Children's Hospital 2013

Journal: :European Journal of Echocardiography 2023

Abstract Funding Acknowledgements Type of funding sources: None. Background/Introduction Propionic acidemia (PA) is an organic acid disorder with poorly described cardiac phenotype despite progressive important remodeling and causes death including congestive heart failure sudden death, often in a setting vigorous exercise or stress. Cardiac modifications begin at cellular level, both metabolic...

2016
Fatma Deniz Aygun Fatih Aygun Halit Cam

Bacillus cereus can cause serious, life-threatening, systemic infections in immunocompromised patients. The ability of microorganism to form biofilm on biomedical devices can be responsible for catheter-related bloodstream infections. Other manifestations of severe disease are meningitis, endocarditis, osteomyelitis, and surgical and traumatic wound infections. The most common feature in true b...

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