OBJECTIVE To study regional blood flow of the striatum in non-ketotic hyperglycaemic choreic patients. METHODS Brain SPECT was performed with intravenous injection of 20 mCi 99mTc hexamethylpropylene amineoxime in six non-ketotic hyperglycaemic choreic patients and 10 age matched patients with a similar level of hyperglycaemia without chorea as a control. The focal perfusion defects were anal...

Abstract Background Chorea hyperglycemia basal ganglia syndrome is a rare disorder causing involuntary movements in both upper and lower limbs. Uncontrolled causes neurotransmitter derangements resulting movements. These cases pose different challenges to anaesthesiologist general regional anaesthesia. Case presentation Here, we discuss case of chorea with limb gangrene posted for knee amputati...

Background: Takayasu’s arteritis (TA) has been associated with many conditions. Herein described is a case of TA in a patient with rheumatic fever complicated with Sydenham’s chorea. Case Report: A 17-year-old female presented at age 6 with rheumatic fever followed by chorea a month later. At the age of 16, she developed a blood pressure discrepancy between the arms and faint pulses. Computed t...

Huntington's chorea is a rare hereditary disorder of the nervous system. It is inherited as an autosomal dominant disorder and is characterized by progressive chorea, dementia and psychiatric disturbances. The best anesthetic technique is yet to be established for these patients with increased risk of aspiration due to involvement of pharyngeal muscles and an exaggerated response to sodium thio...

A family is described with essential non-progressive chorea occurring in an autosomal dominant inheritance pattern over four generations. A few families with an apparently similar disorder have been reported previously. This condition is characterized by early childhood onset of chorea which is not progressive and is compatible with a long life. It is not associated with dementia, seizures, rig...

Senile chorea is a well recognised but poorly understood clinical entity characterised by a slowly progressive, generalised chorea in elderly people without mental deterioration or a clear underlying cause. The Hallervorden-Spatz syndrome is typically thought of as a paediatric condition with extrapyramidal features and dementia. However, it has been described in adults usually presenting with ...

Introduction Fasting plasma tyrosine is raised in hyperthyroidism (Hall, Anderson and Smart, 1969) and serum magnesium levels are low in severe thyrotoxicosis (Marks and Ashraf, 1978). Although tyrosine hydroxylase is the rate-limiting enzyme in the metabolism of tyrosine it is conceivable that more dihydroxyphenylalanine is formed under these conditions which may give rise to choreiform moveme...

various neurological complications occur in primary or secondary antiphospholipid syndrome (aps) consisting of cerebrovascular attacks, ocular events, dementia, seizure, chorea, and transverse myelopathy that are all related to the titer of antiphospholipid antibodies (apl). we report a patient with chorea and retinal vessel occlusion as manifestations of systemic lupus erythematosus (sle) and ...

The case of an elderly patient who had chorea as an initial symptom of systemic lupus erythematosus (SLE) accompanied by antiphospholipid syndrome (APS) is reported. A 68-year-old woman suddenly developed chorea of her left arm and leg. Magnetic resonance imaging (MRI) of the brain demonstrated a focal lesion in the right caudate head, which showed hyperintensity on fluid-attenuated inversion r...