Abstract Amniotic band syndrome (ABS) is not a commonly seen birth defect; however, it may have the potential to be severe and life-threatening requiring adequate attention. We present case of amniotic which encircled head neonate tightly causing deformity. In this report, bilateral Tessier 7 cleft. To our knowledge, most type ABS reported in literature thus far. Level evidence: V, risk / thera...

The diversity of secondary deformities following repair of the cleft lip and nose is striking. The deformities reflect the wide variety of surgical techniques used to repair the cleft lip and the cleft lip nose. Secondary deformities of the repaired cleft lip and nose result from several distinct but related components: congenitally abnormal tissues; surgically modified tissues; the innate tend...

Submucous cleft palate is a specialized subgroup of cleft pathologies, with a worldwide incidence of approximately 1 in 600 live births. Besides the classical triad of bifid uvula, muscle diastasis (zona pellucida) and a notch at the posterior hard palate (defined by Calnan), the anatomical presentation of submucous cleft palate may differ. Unlike overt cleft palate, because of the concealed an...

Composite chondrocutaneous grafts were applied to 12 patients in various forms to repair the columellar deficit, to form the nasal tubercle and nostril sill in cleft lip nose patients. Cleft lip-nose deformity patients with alar cartilage hypoplasia, obtuse angulation of the medial and lateral crura and the resulting plica vestibularis, internal nasal valve problems associated with the weakness...

The association of ectrodactyly (lobster claw deformity or cleft of the hands and feet) and dacrocystitis was first reported by Cockayne in 19361, It was, however, Rudiger and others2 who stressed the association of atypical ectodermal dysplasia with ectrodactyly and cleft lip and palate and suggested the name EEC -syndrome, This is a rare congenital syndrome which shows both a familial autosom...

Tessier cleft no. 30 is a rare congenital anomaly. It may range in severity from median cleft of the upper and lower lip to cleft of the manubrium sterni involving the mandible, floor of the mouth, tongue, hyoid bone, thyroid cartilage and strap muscles. Ankyloglossia and median web in the neck extending from chin resulting in neck contracture are frequently found. This is a case report of medi...

The congenital midline cervical cleft is a rare developmental abnormality of the anterior part of the neck Luschka in 1848 and noted in the English literature by Bailey in 1924 [1,2]. The lesion is often initially evaluated by a pediatrician or primary care physician who may misinterpret the anomaly as a branchial cleft deformity or thyroglossal duct cyst. Although developmentally related to th...

The choice of CPT code first depends upon whether the procedure is primary, secondary or performed for a cleft lip nasal deformity. If the nose has never undergone previous surgery, the procedure is considered primary; if a previous procedure has been performed, whether by you or by another surgeon, then the current operation is considered secondary. Separate codes describe procedures performed...