نتایج جستجو برای: congenital nephrotic syndrome

تعداد نتایج: 719259  

2013
Indra Rani Gupta Cindy Baldwin David Auguste Kevin C H Ha Jasmine El Andalousi Somayyeh Fahiminiya Martin Bitzan Chantal Bernard Mohammad Reza Akbari Steven A Narod David S Rosenblatt Jacek Majewski Tomoko Takano

BACKGROUND Congenital nephrotic syndrome arises from a defect in the glomerular filtration barrier that permits the unrestricted passage of protein across the barrier, resulting in proteinuria, hypoalbuminaemia, and severe oedema. While most cases are due to mutations in one of five genes, in up to 15% of cases, a genetic cause is not identified. We investigated two sisters with a presumed rece...

Journal: :Tạp chí Nghiên cứu và Thực hành Nhi khoa 2018

Journal: :international journal of hematology-oncology and stem cell research 0
mohammadali mashhadi hematology-oncology department, ali-e- ebne abitaleb hospital, zahedan university of medical sciences, zahedan, iran

the hematological malignancies associated with nephrotic syndrome are mainly hodgkin’s and non-hodgkin’s lymphomas and chronic lymphocytic leukemia. acute myelogenous leukemia (aml) has rarely been described in associated with nephritic syndrome. we report a rare case of acute myelogenous leukemia who presented with nephrotic syndrome. a previously healthy 62-year-old man was admitted in nephro...

Journal: :international journal of pediatrics 0
rahime renda antalya research and education hospital, pediatric nephrology department, antalya, turkey. özlem aydoğ ankara dr.sami ulus research and education hospital, pediatric nephrology department, ankara, turkey. mehmet bülbül ankara dr.sami ulus research and education hospital, pediatric nephrology department, ankara, turkey. evrim kargın çakıcı ankara dr.sami ulus research and education hospital, pediatric nephrology department, ankara, turkey.

background and aim: steroid-resistant nephrotic syndrome (srns) accounts for 10%-20% of all cases of idiopathic nephrotic syndrome. these patients are at risk of developing end-stage renal disease. the aim of this study was to determine the demographic characteristics, renal biopsy findings, response to immunosuppressive treatment, and prognosis in pediatric patients with srns.materials and met...

Journal: :Journal of the American Society of Nephrology : JASN 2004
Anne-Tiina Lahdenkari Kari Lounatmaa Jaakko Patrakka Christer Holmberg Jorma Wartiovaara Marjo Kestilä Olli Koskimies Hannu Jalanko

Glomerular epithelial cells (podocytes) play an important role in the pathogenesis of proteinuria. Podocyte foot process effacement is characteristic for proteinuric kidneys, and genetic defects in podocyte slit diaphragm proteins may cause nephrotic syndrome. In this work, a systematic electron microscopic analysis was performed of the structural changes of podocytes in two important nephrotic...

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