C triatriatum is a very rare congenital cardiac anomaly with no known associated genetic abnormalities. Cor triatriatum is generally an isolated anomaly but may be associated with anomalous pulmonary venous return in approximately 10% of patients, patent ductus arteriosus, left superior vena cava, ventricular septal defects, Shone syndrome, tricuspid atresia, Ebstein malformation, atrioventricu...

Classic cor triatriatum is rarely found in adults. Preoperative assessment of classic cor triatriatum in a 22 year old man without symptoms by three dimensional echocardiography was more informative than transoesophageal echocardiography or magnetic resonance imaging, which both showed only a small hole in the membrane separating the accessory atrium from the true left atrium. The size of the h...

We herein present a case of a successful correction of cor triatriatum associated with thrombotic pulmonary hypertension diagnosed in an adult female patient. We confirmed diagnosis using transthoracic and transesophageal echocardiography in addition to cardiac computed tomography and magnetic resonance imaging. Surgical repair comprised excision of the fibromuscular membranous septum in the le...

A 19-year-old female patient was admitted to our hospital with dyspnea, chest pain, and shortness of breath. A chest radiograph showed mild cardiomegaly. Echocardiography revealed an extra chamber in the heart. To evaluate this abnormality, ECG-gated 16-detector-row computed tomography angiography was performed. Multidetector computed tomography (MDCT), showing cor triatriatum with total anomal...

A 45-year-old woman with cor triatriatum sinister was admitted for laparoscopic resection of an ovarian tumor. Her medical history was benign with the exception of a single episode of syncope one year ago. A 1.5-cm membrane fenestration was found on echocardiography, but there were no other cardiac structural anomalies. General anesthesia was established with etomidate, sevoflurane, and remifen...

In the case of cor triatriatum, as in other congenital abnormalities, especially if discovered in adult age, concomitant pathology of the cardiac valves should be carefully investigated. This demands an adequate pre-operative study, today possible with the modern imaging techniques. Here, we report a 19-year-old woman operated for a cor tiatriatum sinister; the typical fenestrated diaphragm was...

COR TRIATRIATUM is an uncommon congenital cardiac anomaly that is characterized by division of the left atrium into two separate chambers by a fenestrated membrane. This condition typically presents in infancy or early childhood, and can be associated with other cardiac anomalies. A smaller number of adult cases have been reported in the literature. We present the case of a patient with cor tri...