Dentinogenesis imperfecta (DI) type II or hereditary opalescent dentin is inherited in simple autosomal dominant mode with high penetrance and low mutation rate. It generally affects both the deciduous and permanent dentitions. DI type II corresponds to a localized form of mesodermal dysplasia, observed in histodifferentiation. Early diagnosis and treatment are therefore, fundamental, aiming at...

Dentinogenesis imperfecta (DI) is a hereditary dentin defect caused by an autosomal dominant mutation in dentin sialophosphoprotein gene. Defective dentin development results in discolored teeth that are prone to wear and fracture. Early diagnosis and proper treatment are necessary to achieve better functional and esthetic results and minimize nutritional deficiencies and psychosocial distress....

A better understanding of the microstructure and mechanical properties enamel dentine may enable practitioners to apply current adhesive dentistry protocols clinical cases involving disorders (dentinogenesis imperfecta or dysplasia). Publications (up June 2020) investigating were browsed in a systematic search using PubMed/Medline, Embase Cochrane Library electronic databases. Two authors indep...