Melanotic neuroectodermal tumor of infancy (melanotic progonoma) is a rare tumor of neural crest origin that is commonly found in the maxilla of infants (1). Brain involvement is rare (2–4). One report cites malignancy in six cases (1). We describe a case of melanotic neuroectodermal tumor that presented as an aggressive skull-based tumor that was resected and later recurred in the posterior fo...

Primitive  neuroectodermal  tumor  (PNET)  of  kidney  is  an  extremely  rare  renal  neoplasm  with only about fifty reported cases in literature.  Presumably,of neural crest origin, these tumors behave  aggressively  and  carry  a  poor prognosis.  We  report  a  case  of  22-year  old  female  patient complaining of left loin pain with recurrent hematuria for last 3 months. On clinical ex...

Extraskeletal Ewing's Sarcoma/Primitive Neuroectodermal Tumor presenting as a breast mass is uncommon. It may pose a diagnostic challenge. In order to increase awareness and identify potential diagnostic pitfalls, we report a 24 year-old woman extraosseous Extraskeletal Ewing's Sarcoma/Primitive Neuroectodermal Tumor arising in the breast.

Primitive neuroectodermal tumor is an invasive neoplasm with neuronal differentiation, which frequently results in metastasis in various organs. We report the case of a patient with primitive neuroectodermal tumor whose primary site was the axilla. The patient presented with metastases in the lung, pleura, bone, iliac muscle and bone marrow. We highlight the uncommon finding in the pleural flui...