نتایج جستجو برای: rara positive apl

تعداد نتایج: 662831  

2012
Emma Lång Stig Ove Bøe

Acute promyelocytic leukemia (APL) is a distinct subtype of acute myeloid leukemia (AML) characterized by a severe bleeding tendency, accumulation of abnormal promyelocytes in the bone marrow and a reciprocal t(15;17) chromosomal translocation that fuses the gene encoding the promyelocytic leukemia protein (PML) to that encoding retinoic acid receptor alpha (RARA) (de Thé & Chen, 2010). During ...

Journal: :Blood 2010
Elizabeth E Gardiner Michael C Berndt

phagic vesicles after treatment with these agents. Functionally, activation of autophagy by the mammalian target of rapamycin (mTOR) inhibitor triggers PML/RARA destabilization in the NB4 APL cell line, resulting in enhanced ATRA-induced differentiation. Conversely, the autophagy inhibitor BafA impedes treatment-induced PML/ RARA degradation and biologic response. These results are important in...

Journal: :Blood 2008
Syed Khizer Hasan Ashley N Mays Tiziana Ottone Antonio Ledda Giorgio La Nasa Chiara Cattaneo Erika Borlenghi Lorella Melillo Enrico Montefusco José Cervera Christopher Stephen Gnanam Satchi Anne Lennard Marta Libura Jo Ann W Byl Neil Osheroff Sergio Amadori Carolyn A Felix Maria Teresa Voso Wolfgang R Sperr Jordi Esteve Miguel A Sanz David Grimwade Francesco Lo-Coco

Therapy-related acute promyelocytic leukemia (t-APL) with t(15;17) translocation is a well-recognized complication of cancer treatment with agents targeting topoisomerase II. However, cases are emerging after mitoxantrone therapy for multiple sclerosis (MS). Analysis of 12 cases of mitoxantrone-related t-APL in MS patients revealed an altered distribution of chromosome 15 breakpoints versus de ...

2001
Philippe Kastner H. Jeffrey Lawrence Caroline Waltzinger Norbert B. Ghyselinck Pierre Chambon Susan Chan

Acute promyelocytic leukemia (APL) is always associated with chromosomal translocations that disrupt the retinoic acid receptor a (RARa) gene. Whether these translocations relate to a role for endogenous RARa in normal granulopoiesis remains uncertain because most studies addressing this question have used nonphysiological overexpression systems. Granulocyte differentiation in cells derived fro...

2004
Edgar G. Rizzatti Fernando L. Portieres Sérgio L.R. Martins Eduardo M. Rego Marco A. Zago Roberto P. Falcão

Acute promyelocytic leukemia (APL) is a subtype acutemyeloid leukemia inwhich leukemic promyelocytes predominate in the bone marrow (BM). Rapid diagnosis is critical for treatment decision since all-trans-retinoic acid must be administrated promptly. The microgranular variant may be of difficult diagnosis, as it may be confused with other diseases on morphological grounds. The purpose of this s...

2012
Min Jin Kim John Jeongseok Yang Claus Meyer Rolf Marschalek Tae Sung Park

which permits unrestricted non-commercial use, distribution, and reproduction in any medium, provided the original work is properly cited. Molecular methods for genomic analyses of variant PML-RARA or other RARA-related chromo-somal translocations in acute promyelocytic leukemia TO THE EDITOR: We read an interesting paper by Palta et al. in a recent issue of the Korean Journal of Hematology tit...

2002
J Collins tomas Ganz

In this issue, both Dong and Tweardy (page 2637) and Maurer et al (page 2647) offer a detailed functional and biochemical characterization of the Stat5b-RARa fusion protein, which was originally described in a patient with acute promyelocytic leukemia (APL) several years ago (Arnould et al, Hum Mol Genetics. 1999;8:1741-1749). Stat5b is one of 5 genes that have now been identified as fusion par...

Journal: :International journal of clinical and experimental pathology 2015
Yuting Tang Ying Wang Liang Hu Fankai Meng Danmei Xu Kai Wan Lifang Huang Chunrui Li Jianfeng Zhou

Acute Promyelocytic Leukemia (APL) is one of the most curable leukemia which shows great sensitivity to all-trans retinoic acid (ATRA) although a small number of the patients present poor prognosis and short survival. Isochromosome 17 in APL which usually bears an additional copy of RARA/PML fusion gene is considered to be a negative factor on its prognosis. Cryptic t(15;17) on i(17q) leads to ...

Journal: :Acta haematologica 2010
Kalliopi N Manola Maria Karakosta Constantina Sambani Georgia Terzoudi Maria Pagoni Eleni Gatsa Maria Papaioannou

Isochromosome of the long arm of the derivative chromosome 17, originating from the translocation t(15;17) [ider(17)(q10)t(15;17) or ider(17q)] in acute promyelocytic leukemia (APL), is a rare chromosome aberration which has been associated with a poor prognosis. In the present study, we report on 4 male APL patients with ider(17q) and review the clinical, cytogenetic and molecular characterist...

1998
Fabien Guidez Sarah Ivins Jun Zhu Mats Söderström Samuel Waxman Arthur Zelent

Typical acute promyelocytic leukemia (APL) is associated with expression of the PML-RARa fusion protein and responsiveness to treatment with all-trans retinoic acid (ATRA). A rare, but recurrent, APL has been described that does not respond to ATRA treatment and is associated with a variant chromosomal translocation and expression of the PLZFRARa fusion protein. Both PMLand PLZF-RARa possess id...

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