sented with progressive gait unsteadiness and hearing loss since the age of 54. Clinical examination showed ataxia and dysarthria together with bilateral profound sensorineural hearing impairment. MRI revealed extensive cerebellar atrophy (predominant in the superior vermis) on T1-weighted images (Fig. A), together with a hypointense rim along cerebral convexities, sylvian and interhemispheric ...

A 41-year-old woman presented with 2 months of dysarthria. Her history included 6 years of unsteadiness resulting in multiple falls and 10 years of intermittent urinary incontinence. She had a history of significant trauma including having been knocked over by a horse and being involved in 2 car accidents, 1 resulting in loss of consciousness and amnesia. On examination, she had finger-nose dys...

BACKGROUND Considered a rare disorder, superficial siderosis of the central nervous system (SSCN) has become more frequently diagnosed in recent years. As it is characterized by progressive sensorineural hearing loss, patients' needs may surpass the capability of hearing aid technology. Despite the retrocochlear nature of the disorder, patients have undergone cochlear implantation (CI) with var...

OBJECTIVE To describe a novel cause of meningeal siderosis due to intermittent subarachnoid bleeding caused by chronic bilateral jugular vein thrombosis. DESIGN Case report and review of literature. PATIENT A 51-year-old man with a distant history of cervical injury who presented with transient aphasia in the setting of progressive cognitive decline. INTERVENTION Neurological examination,...

Abstract Background Regardless of the cause superficial siderosis (SS) disease, which is bleeding, source bleeding cannot be found in some cases. Case presentation In this article, we report two cases with idiopathic SS. 1 presented bilateral hearing loss, cognitive impairment, sleep disturbances, and tremors. 2 sensory neural ataxia, spastic paraparesis. both cases, brain MRI indicated evidenc...