Accepted 19 November 2017 DesCripTion A 3-year-old boy presented with global developmental delay, abnormal craniofacial growth and left focal seizures since infancy. He was the first child of a non-consanguineous couple with unremarkable perinatal period. Family history was non-contributory. On examination, he had macrocephaly (head circumference 55 cm, >3 z-score), extensive port-wine stain di...

Presentation Age-related penetrance is seen in HHT. [2] It does not present at birth but commonly presents with recurrent epistaxis, usually in the teenage years. People with the condition develop mucocutaneous lesions, usually involving the nasal mucosa, lips and tongue. These lesions are sharply demarcated red-purple macules, papules or spider-like lesions comprising a mat of tortuous vessels...

To cite: Abangah G, Rashidbeygi M. BMJ Case Rep Published online: [please include Day Month Year] doi:10.1136/bcr-2013201034 DESCRIPTION A 57-year-old woman presented to the emergency department reporting of fresh rectal bleeding since 3 days ago. She had a history of spontaneous recurrent epistaxis since childhood but had never been fully evaluated. Her family history was also notable for a so...

A generalised Weber function is given by wN (z) = η(z/N)/η(z), where η(z) is the Dedekind function and N is any integer; the original function corresponds to N = 2. We classify the cases where some power w N evaluated at some quadratic integer generates the ring class field associated to an order of an imaginary quadratic field. We compare the heights of our invariants by giving a general formu...

Weber Christian disease or idiopathic lobular panniculitis is a skin condition that features recurring inflammation in the fat layer of the skin. We report a case of a 17 year old boy with Weber Christian disease as its occurence is extremely rare with only sparse case reports available, who presented with eighteen-month history off fever with chills off and on, arthralgia predominantly of the ...

Osler–Weber–Rendu syndrome, also known as Hereditary Hemorrhagic Telangiectasia (HHT), is an autosomal dominant disorder. Telangiectasias and Arterio-Venous Malformations (AVMs) are vascular lesions present in HHT, most commonly causing epistaxis and gastrointestinal bleeding. While epistaxis presents as early as childhood, the gastrointestinal manifestations of HHT develop with increasing age.

Weber Christian disease, an idiopathic relapsing febrile subcutaneous and visceral panniculitis is a rare disease in children. We report a case of Weber Christian disease for he first time from Kanti Children's Hospital.

Good heuristic solutions for large Multisource Weber problems can be obtained by solving related p median problems in which potential locations of the facilities are users locations and then solving Weber problems for the sets of users of each facility

Christoph Merkle, Philipp Schreiber and Martin Weber⇑ Merkle is an associate professor of finance at Aarhus University a research fellow the Danish Finance Institute. full Esslingen University. Weber senior Mannheim CEPR. corresponding author: cmerkle{at}econ.au.dk