نتایج جستجو برای: clc

تعداد نتایج: 2349  

Journal: :Molecular medicine reports 2013
Hong Wei Wang Ya Juan Zheng

The chloride channel protein 2 (CLC‑2) is important in maintaining the volume of trabecular meshwork cells by adjusting the outflow of aqueous solutions and maintaining the fluid balance. However, little is known concerning the functions of CLC‑2 in the cytoskeleton, specifically in human trabecular meshwork (HTM) cells. In the present study, two CLC-2 specific siRNAs (siRNA1 and siRNA2) that t...

2013
Miao Miao Bi Sen Hong Hong Yan Zhou Hong Wei Wang Li Na Wang Ya Juan Zheng

Chloride channels (ClCs) have gained worldwide interest because of their molecular diversity, widespread distribution in mammalian tissues and organs, and their link to various human diseases. Nine different ClCs have been molecularly identified and functionally characterized in mammals. ClC-2 is one of nine mammalian members of the ClC family. It possesses unique biophysical characteristics, p...

Journal: :Proceedings of the National Academy of Sciences of the United States of America 2004
Holger Pernice Placido Garcia Helge Willner Joseph S Francisco Franklin P Mills Mark Allen Yuk L Yung

For two decades, the peroxychloroformyl radical, ClC(O)OO, has played a central role in models of the chemical stability of the Venus atmosphere. No confirmation, however, has been possible in the absence of laboratory measurements for ClC(O)OO. We report the isolation of ClC(O)OO in a cryogenic matrix and its infrared and ultraviolet spectral signatures. These experiments show that ClC(O)OO is...

Journal: :Blood 1988
A M Dvorak L Letourneau G R Login P F Weller S J Ackerman

The Charcot-Leyden crystal (CLC) protein is a unique constituent of eosinophils and basophils. This protein forms the hexagonal bipyramidal crystals observed in tissues at sites of eosinophil accumulations, possesses lysophospholipase activity (lysolecithin acylhydrolase E.C.3.1.1.5), and comprises an estimated 7% to 10% of total eosinophil protein. The ultrastructural localization of CLC prote...

Journal: :Human molecular genetics 1999
O Devuyst P T Christie P J Courtoy R Beauwens R V Thakker

Dent's disease, which is a renal tubular disorder characterized by low molecular weight proteinuria, hypercalciuria and nephrolithiasis, is associated with inactivating mutations of the X-linked chloride channel, CLC-5. However, the manner in which a functional loss of CLC-5 leads to such diverse renal abnormalities remains to be defined. In order to elucidate this, we performed studies to dete...

2016
Stacey M. Anderson Dan Raghinaru Jordan E. Pinsker Federico Boscari Eric Renard Bruce A. Buckingham Revital Nimri Francis J. Doyle Sue A. Brown Patrick Keith-Hynes Marc D. Breton Daniel Chernavvsky Wendy C. Bevier Paige K. Bradley Daniela Bruttomesso Simone Del Favero Roberta Calore Claudio Cobelli Angelo Avogaro Anne Farret Jerome Place Trang T. Ly Satya Shanmugham Moshe Phillip Eyal Dassau Isuru S. Dasanayake Craig Kollman John W. Lum Roy W. Beck Boris Kovatchev

OBJECTIVE To evaluate the efficacy of a portable, wearable, wireless artificial pancreas system (the Diabetes Assistant [DiAs] running the Unified Safety System) on glucose control at home in overnight-only and 24/7 closed-loop control (CLC) modes in patients with type 1 diabetes. RESEARCH DESIGN AND METHODS At six clinical centers in four countries, 30 participants 18-66 years old with type ...

Journal: :American journal of physiology. Cell physiology 1998
Tetsushi Furukawa Takehiko Ogura Yoshifumi Katayama Masayasu Hiraoka

In the Xenopus oocyte heterologous expression system, the electrophysiological characteristics of rabbit ClC-2 current and its contribution to volume regulation were examined. Expressed currents on oocytes were recorded with a two-electrode voltage-clamp technique. Oocyte volume was assessed by taking pictures of oocytes with a magnification of ×40. Rabbit ClC-2 currents exhibited inward rectif...

2015
Jongkyu Choi Kirkwood E. Personius Marino DiFranco Warunee Dansithong Carl Yu Saumya Srivastava Donald M. Dixon Darshan B. Bhatt Lucio Comai Julio L. Vergara Sita Reddy

UNLABELLED Loss of Muscleblind-like 1 (Mbnl1) is known to alter Clc-1 splicing to result in myotonia. Mbnl1(ΔE3/ΔE3)/Mbnl3(ΔE2) mice, depleted of Mbnl1 and Mbnl3, demonstrate a profound enhancement of myotonia and an increase in the number of muscle fibers with very low Clc-1 currents, where gClmax values approach ~ 1 mS/cm(2), with the absence of a further enhancement in Clc-1 splice errors, a...

2010
Patrick Schulz Johannes Werner Tobias Stauber Kim Henriksen Klaus Fendler

BACKGROUND ClC-7 is a ubiquitous transporter which is broadly expressed in mammalian tissues. It is implied in the pathogenesis of lysosomal storage disease and osteopetrosis. Because of its endosomal/lysosomal localization it is still poorly characterized. METHODOLOGY/PRINCIPAL FINDINGS An electrophysiological characterization of rat ClC-7 using solid-supported membrane-based electrophysiolo...

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