CONTEXT Dysplastic pulmonary valve stenosis is a less common variety of valvular pulmonary stenosis. It is known to be part of Noonan syndrome. Bony hand anomalies in patients of pulmonary stenosis are very rare. CASE REPORT A 50-year-old lady, with no significant past history, presented with slowly progressive breathlessness and fatigue, and had progressed from NYHA class 1 to 2 over 2 years...

introduction tetralogy of fallot (tof) in the absent of pulmonary valve is a rare congenital anomaly (3%of tof patients). case presentation we are presenting an 18- year-old male with history of dyspnea on exertion and cyanosis since childhood. despite the diagnosis of congenital heart disease, no intervention was done due to his poor socioeconomic culture. at age of 18, he referred to our cent...

Background: Mechanisms and clinical manifestations of coronary artery complications after right ventricular outflow tract reconstruction surgery are not well known. Methods: Patients who had pulmonary valve replacement or the Rastelli procedure at a single tertiary centre were retrospectively analysed. Results: Coronary identified in 20 patients underwent surgery. The median age diagnosis compl...

UNLABELLED The aim of the study was to investigate the occurrence, pattern and clinical aspects of congenital heart diseases and their management in Cameroon. In this multicentred retrospective study from January 2006 till November 2009, out of 51,636 consulting in three referral centres, 505 were recruited. All the patients presented with the following symptoms: cyanosis, clubbing, frequent re...

OBJECTIVE To determine the incidence and prognosis of congenital aortic valve stenosis in the five Health Districts of Liverpool that make up the Merseyside area. DESIGN The records of the Liverpool Congenital Malformations Registry and the Royal Liverpool Children's Hospital identified 239 patients (155 male, 84 female) born with aortic valve stenosis between 1960 and 1990. Patients were tra...

During the past several years therapeutic catheterization techniques have been developed to provide nonsurgical treatment for children with congenital aortic valve stenosis,',2 subvalvar aortic sten o ~ i s , ~ mitral s ten~s is ,~ ,~ and coarctation of the a ~ r t a . ~ , ~ Transcatheter therapy is now generally regarded as the treatment of choice for children with valvar pulmonic stenosis, pu...

NATURAL OCCURRENCE Although there is little data on the exact incidence of poststenotic dilatation, it is common with some types of constriction such as pulmonary and aortic valve stenoses' but rare with others such as infundibular pulmonary stenosis" or supravalvular aortic stenosis. It occurs with both congenital" and acquired' 6 aortic stenosis. Skandalakis et al., in a survey of the literat...

A family with congenital hepatic fibrosis (CHF) and congenital heart disease (CHD) is presented. The consanguineous healthy parents gave birth to 12 children of whom 10 survived. One son had CHF and CHD, one daughter had CHF and a second daughter had CHD. Three other siblings probably had small a ventricular septal defect and another one probably had mild pulmonary valve stenosis. Development o...

A three year old girl with severe congenital mitral stenosis was successfully treated by percutaneous balloon dilatation of the mitral valve. Cardiac catheterisation and cross sectional and Doppler echocardiography indicated that the orifice of the mitral valve had doubled in area. A small atrial septal defect was found at follow up cardiac catheterisation and angiography. Balloon dilatation of...

Described herein are five patients who had double left-sided cardiac valve replacement for mitral and aortic valve stenosis resulting from two different etiologies: rheumatic heart disease, the cause of the mitral stenosis, and congenital heart disease (bicuspid valve), the underlying cause of the aortic stenosis.