نتایج جستجو برای: gdap1

تعداد نتایج: 91  

2017
Chi-Chun Ho Shuk-Mui Tai Edmond Chi-Nam Lee Timothy Shin-Heng Mak Timothy Kam-Tim Liu Victor Wai-Lun Tang Wing-Tat Poon

Charcot-Marie-Tooth disease (CMT) is a common inherited peripheral neuropathy affecting up to 1 in 1214 of the general population with more than 60 nuclear genes implicated in its pathogenesis. Traditional molecular diagnostic pathways based on relative prevalence and clinical phenotyping are limited by long turnaround time, population-specific prevalence of causative variants and inability to ...

2014
Christina DiVincenzo Christopher D Elzinga Adam C Medeiros Izabela Karbassi Jeremiah R Jones Matthew C Evans Corey D Braastad Crystal M Bishop Malgorzata Jaremko Zhenyuan Wang Khalida Liaquat Carol A Hoffman Michelle D York Sat D Batish James R Lupski Joseph J Higgins

We report the frequency, positive rate, and type of mutations in 14 genes (PMP22, GJB1, MPZ, MFN2, SH3TC2, GDAP1, NEFL, LITAF, GARS, HSPB1, FIG4, EGR2, PRX, and RAB7A) associated with Charcot-Marie-Tooth disease (CMT) in a cohort of 17,880 individuals referred to a commercial genetic testing laboratory. Deidentified results from sequencing assays and multiplex ligation-dependent probe amplifica...

Journal: :Neuro-oncology 2023

Abstract BACKGROUND The polio:rhinovirus chimera, PVSRIPO, and the herpes simplex virus, G207, are viral immunotherapies with promising results in Phase I trials of pediatric high-grade glioma (pHGG) medulloblastoma. While some patients have durable responses, others no benefit. purpose this study is to identify genes that putatively confer resistance immunotherapy. METHODS A panel medulloblast...

Journal: :Journal of neurology, neurosurgery, and psychiatry 2004
M Donaghy

I dentification of neurological disease genes has expanded and transformed the neurologist’s nosology in the last decade. Yet some clinicians see the resultant overload of detail as merely making the diagnosis and management of patients more cumbersome with little tangible benefit. Using the example of inherited peripheral neuropathy it is timely for a clinician’s perspective of where neurogene...

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