herlyn-werner-wunderlich (hww) syndrome is an uncommon combined müllerian duct anomalies (mdas) and mesonephric duct malformation of female urogenital tract characterized by uterus didelphys and obstructed hemi-vagina and ipsilateral renal agenesis (ohvira) syndrome. we present a rare and unusual case of this syndrome in a 19 year-old female who suffered from hypomenorrhoea and abdominal pain. ...

Abstract Objective Herlyn-Werner-Wunderlich (HWW) Syndrome, also known as Obstructed Hemivagina and Ipsilateral Renal Anomaly (OHVIRA) syndrome, is a very rare congenital urogenital tract anomaly. The incidence of the syndrome less than 1/1,000,000 females. OHVIRA radiologically presents Wunderlich triad: uterus didelphys, obstructed hemivagina ipsilateral renal agenesis. Clinical presentation ...

Background: Mostyn Embrey syndrome is a rare disorder associated with unilateral renal agenesis and malformations of the female reproductive tract. Delayed diagnosis serious diagnostic difficulties that may lead to inappropriate management including harmful surgery. The aim this paper present imaging studies case number 506 which was first in Iraq, originally reported 2016. Ethics naming syndro...

We read the case report by Rabani and enjoyed it (1). As he said the imperforated hymen is a rare cause of urinary retention in female patients, especially before menarche, but we would like to add some additional comments and suggestions on this issue. The hymen, which is a mesodermal sheet, should be perforated in the late time of the embryonic period but sometimes it does not happen. This ph...

Müllerian agenesis occurs in 1 out of every 4,000–10,000 females. The most common presentation of müllerian agenesis is congenital absence of the vagina, uterus, or both, which also is referred to as müllerian aplasia, Mayer–Rokitansky–Küster–Hauser syndrome, or vaginal agenesis. Satisfactory vaginal creation usually can be managed nonsurgically with successive vaginal dilation; however, there ...

Herlyn–Werner–Wunderlich syndrome (HWWS) is a congenital Müllerian duct anomaly characterized by uterine didelphys, obstructed hemivagina, and ipsilateral renal agenesis. Little is reported about spinal deformity associated with this syndrome. This study presents a case of scoliosis occurring in the setting of HWWS and explores the possible association between the 2 diseases. A previously unrep...

The study of the possible genetic causes complex genital malformations is a subject great interest both to know its etiology and diagnosis for best reproductive advice in these patients. Recently, Chen et al. (1Chen N. Zhao S. Jolly A. Wang L. Pan H. Yuan J. al.Perturbations genes essential Müllerian duct Wölffian development Mayer-Rokitansky-Küster-Hauser syndrome.Am J Hum Genet. 2021; 108: 1-...