Renal Lymphangiectasia (RLM) is a very infrequent benign lymphatic disorder. RLM often misdiagnosed for other disorders suchas cystic renal masses, usually polycystic kidneys. Although parenthetically found in different cases, probable cause of renalfailure and hypertension undiagnosed victims. The etiology unclear results from the formation masses anddilatation perinephric channels. In sinus, ...

A unique clinical case of a combination malformations the anterior abdominal wall (omphalocele large size) and malformation lymphatic system (congenital chyloperitoneum) is presented. Each these defects can lead to fatal outcome, them has greatly increased risk developing an unfavourable outcome. The use immunosuppressive therapy with Sirolimus used for first time during newborn period made it ...

Sirenomelia also called mermaid syndrome is a congenital, rare, lethal, multisystemic human malformation of unknown etiology. The characteristic feature sirenomelia the fusion lower limbs, resulting in appearance mermaid’s tail, and thus name “mermaid syndrome.” This condition characterized by various severe urogenital abnormalities presence singular umbilical cord blood vessel, it more common ...

OBJECTIVE To describe a classification of microcystic lymphatic malformations of the tongue and to investigate different treatment methods. DESIGN Retrospective review of patients treated for microcystic lymphatic malformations of the tongue. Lymphatic malformations were classified into the following 4 groups according to their extent: isolated superficial microcystic lymphatic malformations ...

Epidermal nevi are cutaneous hamartomas developing from ectoderm and one of their types is verrucous epidermal nevus. During the neonatal period, they are pink or slightly pigmented and velvety. Later, they darken and the surface become more warty. When lesions are distributed on one side of body, it is termed nevus unis lateralis. Lymphangioma is a lymphatic malformation which manifests with f...

Lymphatic malformation (LM) is an abnormal collection of lymphatic fluid within cysts or channels. LM can occur in any part the body, but leading to scrotal swelling very rare, and this unusual location often leads diagnostic errors because most common cause a cystic lesion hydrocele. In case presented here, previously healthy 3-year-old boy recently developed left clinically mimicking communic...

Combined/complex malformations Klippel-Trenaunay syndrome (capillary-lymphatico-venous malformation) Proteus syndrome Maffucci syndrome Table 110.1: Classification of lymphatic malformations. Introduction Lymphangiomas are developmental defects of the lymphatic channels that belong to a large spectrum of vascular malformations. They are most commonly located in the head and neck region, and to ...