A 75-year-old woman presented with dyspnea on exertion, orthopnea, paroxysmal nocturnal dyspnea, and edema. Macroglossia, generalized petechiae, raccoon eyes sign, and peripheral neuropathy were present, and an echocardiogram showed cardiac dilatation and left ventricular systolic dysfunction. Rectal biopsy and immune fixation electrophoresis confirmed the diagnosis of AL amyloidosis.

The case of a 37-year-old woman with lipoid proteinosis is presented. The first symptoms of hoarseness of voice occurred in puberty. Additional symptoms included beaded eyelid papules, macroglossia with yellowish papules, yellowish deposits of soft palate, popular eruption in the axillary area and tuberous nodules on the elbows.

1. Thompson JN, Gibson B, Kohut RI: Airway obstruction in LeFort fractures. Laryngoscope 1997; 97:275-9 2. Gotta AW: MaXilhfacial trauma, Textbook of Trauma Anesthesia and Critical <:are. Edited by Christopher M. Grande. Missouri, Mosby Year-Book Inc., 1993, pp 529-39 3 . Schultz KC: Nasotracheal intubation in the presence of Eicial fractures. Plast Reconstr Surg 1990; 86: I046 4. Gordon NC, To...

developmental disturbances of the tongue (aglossia, macroglossia, microglossia, and ankyloglossia) can adversely affect the development of the surrounding structures including the palate, alveolar process, and teeth. these developmental disturbances impair functions such as mastication, speech, and swallowing. ankyloglossia is of various types and may be associated with other syndromic features...