نتایج جستجو برای: mitochondrial encephalomyopathy

تعداد نتایج: 132426  

2005
Mark Paller Fred Silva Fred Hsieh Reginald Gohh Lance Dworkin

MELAS (mitochondrial encephalomyopathy with lactic acidosls and stroke-like episodes) is one of a group of heterogeneous yet clinically distinct syndromes ascribed to a defect in mitochondrial function. Here, the case of a patient diagnosed with the 1 Received November 21, 1994. Accepted October 19. 1995. 2 Correspondence to Dr. L Dworkin, Division of Renal Diseases, The Rhode Island Hospital, ...

Journal: :Arquivos de neuro-psiquiatria 2007
Adriana Bastos Conforto Fabio Iuji Yamamoto Sueli Mieko Oba-Shinjo Julio Guy C Pinto Maurício Hoshino Milberto Scaff Suely Kazue Nagahashi Marie

PURPOSE It has been suggested that mitochondrial disease may be responsible for a substantial proportion of strokes of indetermined origin. We have preliminarily screened for MELAS (mitochondrial encephalomyopathy, lactic acidosis, and stroke-like episodes) mutations in young patients with cryptogenic strokes. METHOD The mitochondrial mutations A3243G and T3271C were investigated in 38 subjec...

Journal: :Genetics 2007
Wensheng Liu Radhakrishnan Gnanasambandam Jeffery Benjamin Gunisha Kaur Patricia B Getman Alan J Siegel Randall D Shortridge Satpal Singh

Mitochondrial dysfunction is involved in many neurodegenerative disorders in humans. Here we report mutations in a gene (designated levy) that codes for subunit VIa of cytochrome c oxidase (COX). The mutations were identified by the phenotype of temperature-induced paralysis and showed the additional phenotypes of decreased COX activity, age-dependent bang-induced paralysis, progressive neurode...

Journal: :Diagnostic and interventional radiology 2013
Gökçen Çoban Savaş Göktürk Erkan Yildirim Zuhal Çalışkan Bahriye Horasanli Hatice Aysun Akça

Mitochondrial neurogastrointestinal encephalomyopathy (MNGIE) is a rare multisystemic autosomal recessive disorder characterized by ptosis, gastrointestinal dysmotility, cachexia, peripheral neuropathy, and leukoencephalopathy. We aimed to raise awareness in radiologists regarding this difficult-to-diagnose syndrome, which occurs in the presence of coexistent gastrointestinal dysmotility, cache...

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