نتایج جستجو برای: nphs2

تعداد نتایج: 351  

2009
Soo Jin Park Byung Ha Lee Dae Joong Kim

PURPOSE As a membrane protein at the insertion site of the slit diaphragm (SD) complex in podocyte foot processes, podocin has been reported to act as a scaffolding protein required to maintain or regulate the structural integrity of the SD. In order to identify proteins that associate or interact with podocin, we screened a mouse kidney complementary DNA (cDNA) library using a yeast 2-hybrid s...

2017
Mansoureh Tabatabaeifar Tanja Wlodkowski Ivana Simic Helga Denc Geraldine Mollet Stefanie Weber John Julius Moyers Barbara Brühl Michael Joseph Randles Rachel Lennon Corinne Antignac Franz Schaefer

Mutations in the NPHS2 gene, encoding podocin, cause hereditary nephrotic syndrome. The most common podocin mutation, R138Q, is associated with early disease onset and rapid progression to end-stage renal disease. Knock-in mice carrying a R140Q mutation, the mouse analogue of human R138Q, show developmental arrest of podocytes and lethal renal failure at neonatal age. Here we created a conditio...

2013
Markus Gödel Benjamin N. Ostendorf Jessica Baumer Katrin Weber Tobias B. Huber

Mutations in the gene NPHS2 are the most common cause of hereditary steroid-resistant nephrotic syndrome. Its gene product, the stomatin family member protein podocin represents a core component of the slit diaphragm, a unique structure that bridges the space between adjacent podocyte foot processes in the kidney glomerulus. Dislocation and misexpression of slit diaphragm components have been d...

Journal: :Physiological research 2013
H Lu L L Chen X Y Jiang Y Mo Y H Ling L Z Sun

We used a rat model to assess the role of nephrin, podocin, and desmin in the pathogenesis of IgA nephropathy (IgAN). A rat IgAN model was established by administration of BSA, CCl(4), and lipopolysaccharide (LPS) and compared with healthy control rats. Urinary protein, urine red blood cells, and biochemical parameters were measured for 12 weeks. Renal morphology and ultrastructure were examine...

2013
Stavros Stratakis Kostas Stylianou Ioannis Petrakis Vasiliki Mavroeidi Rafaela Poulidaki Christina Petra Demitrios Moisiadis Spyros Stratigis Eleftheria Vardaki Lydia Nakopoulou Eugene Daphnis

OBJECTIVE Recent studies have shown a beneficial effect of rapamycin in passive and active Heymann Nephritis (HN). However, the mechanisms underlying this beneficial effect have not been elucidated. METHODS Passive Heymann Nephritis (PHN) was induced by a single intravenous infusion of anti-Fx1 in 12 Sprague-Dawley male rats. One week later, six of these rats were commenced on daily treatment...

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