conclusions children with chd are at risk of severe complications with the involvement of other organs. long-term febrile illness should be taken seriously in these children. they need hospitalization and careful evaluation. case presentation a 6-year-old girl with a ventricular septal defect (vsd) was presented. echocardiography revealed large vegetation in the right ventricular outflow tract ...

pulmonary alveolar proteinosis, (pap) is a rare disease of unknown etiology, characterized by accumulation of intra-alveolar proteinaceous material which is rich in lipid and positive on periodic acid-schiff stain. two clinically different pediatric types have been defined as congenital pap which is fulminant and fatal, and a late-onset pap which is similar to the adult form and less severe. ei...

unilateral pulmonary artery agenesis (upaa) is a rare congenital anomaly during the 4 th  week of gestational age. it is defined as an absence of pulmonary parenchyma and its supporting artery. a 9-year-old girl was admitted to our hospital because of chronic cough. chest examination showed a decrement in lung sound of right hemi-thorax with expiratory wheeze. chest radiography (cxr) revealed a...

conclusions pcm has not been reported in iran until now, but it should be considered as a differential diagnosis when risk factors or symptoms of pcm are detected. case presentation a 72-year-old man had a four-year history of dyspnea, dry cough, and weakness and a recent weight loss of more than 10 kg. first, he was treated with glucocorticoid, but he did not continue this treatment. core need...

wegener’s granulomatosis is a necrotizing granulomatous vasculitis involving small and medium sized vessels. the syndrome is classically defined as having involvement of kidney, lungs and upper respiratory tract (i.e. sinuses). wegener’s granulomatosis may be present in other autoimmune or inflammatory diseases, particulary systemic lupus erythematosis (sle), but most frequently has been associ...

pulmonary metastases occur in 30% of all oncology patients. surgical resection of lung metastases is a widely accepted procedure but long-term results are disappointing with a 5-year survival rate of 20-40% and the results vary with the histologic type of the primary tumor. due to unavailability of any study regarding pulmonary metastasectomy in iran and emergence of new treatment modalities, r...

background: hydatid disease is a major world health problem and pulmonary hydatidosis is a widespread disease. it is presented with different clinical manifestations. in order to determine the most clinical manifestation, diagnostic methods and clinical outcome in our patients, we conducted this study. methods : forty-nine patients with pulmonary hydatid cysts who were admitted to our hospital ...

background: to determine the mean and median delays in pulmonary tuberculosis (ptb) diagnosis among adults in one of the world’s highest gross domestic product per capita countries and identify patient and health system‑related reasons for these delays. methods: this is a cross‑sectional, face‑to‑face, prospective study of 100 subjects with confirmed ptb, conducted at main tuberculosis (tb) adm...

the purpose of this study was to evaluate the characteristics of anthracofibrosis and the relationship between bronchial anthracofibrosis (baf) and tuberculosis during autopsy in the iranian legal medicine organization (lmo). in this cross-sectional study, 385 subjects who had died from 2007 to 2010 were examined. a questionnaire having information such as the deceased's age, sex, ethnicity, sm...

Background: Alveolar hypoxia induces monophasic pulmonary vasoconstriction in vivo, biphasic vasoconstriction in the isolated pulmonary artery, and controversial responses in the isolated perfused lung. Pulmonary vascular responses to sustained alveolar hypoxia have not been addressed in the isolated perfused rat lung. In this study, we investigated the effect of sustained hypoxic ventilation o...