Background This study aimed to investigate diverse structure of pulmonary blood vessels in patients with combined pulmonary atresia and ventricular septal defect and examine the effect on surgery result. Materials and Methods This cohort retrospective study was conducted on admitta...

Aortic valve atresia is a common feature of hypoplastic left heart syndrome, which consists of various degrees of underdevelopment of the left ventricle aorta complex; nevertheless it can also be associated with a large ventricular septal defect (VSD) and a rather developed left ventricle. Atresia of the aortic valve prevents antegrade blood flow from the left ventricle to the ascending aorta, ...

Eighteen cases of mitral atresia with normal aortic valve plus 68 cases from the literature are analyzed. A new classification based on anatomical findings is proposed. Pulmonary stenosis or atresia is frequent in the type with transposition of the great arteries. The rare instances of normal or large left ventricle are due to a large ventricular septal defect, or to straddling or displaced tri...

Microanigiographlic examinatioin of the pulmoniary arterial svstem in 12 n1ewborn in1fants with conicomitanit steniosis or atresia of the aortic anid mitral orifices showed that the intrapulmonary arterial pattern is inifluenced by the state of the forameni ovale. In inifanlts with aortic atresia with a prematuirely closed foramein ovale, that is cases in which the left side of the heart is a c...

A twenty-three-year-old male truck driver with a 12-pack year smoking history and no previous of hospitalization was admitted to the “Shefqet Ndroqi” University Hospital pulmonology department after cardiologist consultation where he diagnosed pulmonary hypertension. Two patient’s uncles from his mother’s side died during their pediatric age congenital heart defects. contrast-enhanced chest com...

The present report describes a male newborn with a pulsatile structure beneath the sternum. Echocardiography showed common atrium, a single ventricle, mitral atresia, double outlet right ventricle, subpulmonary stenosis, small pulmonary artery branches, and a thin walled ventricular diverticulum suggestive of Cantrell's syndrome. The diverticulum was resected to prevent life threatening events ...

THE GENESIS OF COMMUNICATIONS between the right ventricle and coronary arteries commonly associated with pulmonary atresia remains uncertain. Edwards' attributed the persistence of these communicating sinusoids to increased right ventricular pressure and emphasized the importance of right ventricular outflow obstruction, intact ventricular septum, and competence of the tricuspid valve. Other au...

Tetralogy of Fallot (TOF) is the commonest congenital cyanotic heart disorder, accounting for 5–6 % of them [1]. It is characterized by a large ventricular septal defect, right ventricular outflow tract obstruction, right ventricular hypertrophy, and aorta overriding the interventricular septum. Most patients with TOF undergo reparative surgery in childhood. TOF with pulmonary atresia is the ex...

Congenital tricuspid atresia has been classified into two groups, those with and those without transposition of the great vessels (Kiihne, 1906). Each of these groups is further subdivided according to whether there is an increase or a decrease in the pulmonary blood flow (Edwards and Burchell, 1949). Tricuspid atresia with transposition of the great vessels and an increase in pulmonary blood f...

Four hearts are described in which the right atrioventricular valve, draining a morphologically right atrium, straddled and overrode a septum between a right-sided chamber of left ventricular morphology and a left-sided chamber of right ventricular morphology. The degree of override varied between the straddling valve and was committed by 20-45% to the morphologically right ventricle. The ventr...