persistent mullerian duct syndrome in a 71-year-old man, case report h. salehi md , m.r. vatani baf md received:27/06/06 sent for revision: 11/10/06 received revised manuscript: 07/02/07 accepted: 12/02/07 background and objective: normal sexual differentiation occurs in the 6th embryonic week and in a normal embryonic life. both wolffian and mullerian ducts are present until the onset of sexua...

A 12-year-old boy with the Pfeiffer syndrome presented with nonpalpable testes. Medical history was significant for multiple operations to correct bicoronal craniosynostosis, hypertelorism and syndactyly of the hands. Physical examination revealed no palpable gonads in the scrotum or inguinal canals. However, virilization and development of secondary sex characteristics had begun. Plasma testos...

Persistent Müllerian duct syndrome (PMDS) is a rare, sex-limited, autosomal recessive disorder representing male pseudo-hermaphroditism. It is observed in males with the presence of female reproductive organs such as the uterus, cervix, and bilateral fallopian tubes along with normally developed male reproductive organs. It generally occurs during embryogenesis due to mutation in anti-Müllerian...

Background: Cryptorchidism is one of the most common genitourinary disorders in young boys. About 1% 2% of boys at age of 1 year have an undescended testis (UDT); this disorder is unilateral in about 90% of individuals and bilateral in about 10%. However, bilateral impalpable testes represent a special category that should be differentiated from anorchidism as well as male pseudohermaphroditism...

Introduction and Aims. Congenital absence of the vas deferens is an uncommon anomaly and this clinical condition is responsible for up to 1-2% of male infertility. It can be either unilateral or bilateral and the associated anomalies include cryptorchidism, seminal vesicles and ejaculatory ducts anomalies, and renal anomalies such as renal agenesis. We hereby present a case of congenital unilat...

Ectopic penis is usually associated with penoscrotal transposition, and it is rarely observed in isolation. We report a surgical approach for an extremely rare case. A 10-year-old male patient with bilateral cryptorchidism and ectopic penis and scrotum in perineal area, with no penoscrotal transposition, representing an association not yet described in literature. A previous orchiopexy failed d...

Cryptorchidism, or maldescended testis, is a common problem encountered in pediatric age groups. Despite more than 100 years of research, many aspects of cryptorchidism are not well defined and remain controversial. However, cryptorchidism clearly has deleterious effects on the testis over time.(1-4)Among the problems associated with an undescended testis are an increased risk for testicular tu...