Budd-Chiari syndrome is an uncommon disorder characterized by the thrombotic or non-thrombotic obstruction of hepatic venous outflow anywhere along the venous course from the hepatic venules to the junction of the inferior vena cava and the right atrium. The etiology of Budd-Chiari syndrome is classified as primary, attributable to intrinsic intraluminal thrombosis or the development of venous ...

Recently, Iskandar et al described "Chiari Zero malformation" to characterize some kind of syringomyelia that exhibits classic Chiari-type symptoms with little to no herniation, but there is some dilemma about whether it is actually present. We presented a 38-year-old-man with a diagnosis of cervical syringomyelia. In his neurological examination, there was monoparesia at the left leg together ...

Chiari malformation is a congenital anomaly that primarily involves the downward displacement of the cerebellar tonsils through the foramen magnum and elongation of forth ventricle and lower brainstem. Patients with Chiari I (congenital or acquired) malformation are asymptomatic or may present with neurologic signs and symptoms. It is always a question of safety of neuraxial anesthesia in these...

Budd-Chiari syndrome has been described as a late complication of Behçet's disease. Although the mortality rate associated with Behçet's disease is low, it can escalate in the presence of Budd-Chiari syndrome and may be further complicated by intracardial thrombus formation. It is therefore important to detect and initiate management early in the disease course. The imaging modalities of choice...

Address for Correspondence: Dr. Joseph Abraham, Department of Anatomy, Government Medical College and Hospital, Chandigarh 32, India, 160030. Phone No.: +919041466127. E-Mail: [email protected] Chiari malformations (CM) are named for Hans Chiari, an Austrian pathologist, who first identified type I-III in 1891. This study was conducted on 400 fetuses obtained from department of Obstetrics an...

Cerebral computed tomography (CT) is the primary imaging modality in the investigation of suspected cerebellar degeneration. A case is presented in which an inaccurate clinical and radiologic diagnosis of olivo-pontocerebellar degeneration resulted from CT imaging demonstrating loss of cerebellar substance. Subsequent clinical recognition of downbeat nystagmus led to a diagnosis of Chiari malfo...

Chiari I malformation may not be congenital, but may be acquired as a consequence of skull deformities and other associated intracranial factors in patients with craniosynostosis. Pfeiffer syndrome is one of the many conditions associated with Chiari I malformation. Premature fusion of multiple cranial sutures and cloverleaf skull (kleeblattschädel deformity) are often observed in the calvaria ...

We report a child with osteopetrosis, oxycephaly and Chiari type I malformation who presented with raised intracranial pressure. During cranial expansion surgery the patient developed sudden cardiac arrest which we believe was probably related to the Chiari malformation. The case highlights a previously unrecognized association between osteopetrosis, craniosynostosis and a persistently open fon...