نتایج جستجو برای: frameshift mutation

تعداد نتایج: 291994  

Journal: :Cancer research 1998
J C Boyer R A Farber

Dinucleotide repeats, because of their repetitive nature, are prone to frameshift mutations, most likely via a DNA-polymerase slippage mechanism. Mutation rates in microsatellite DNA sequences are high in mismatch repair-defective cells. In normal cells, only estimates of maximal rates of mutation in microsatellites have been possible previously, because of the low sensitivity of screening assa...

Journal: :Current Biology 1995
R. E. Lenski P. D. Sniegowski

Adaptive frameshift mutations in the lacZ gene of Escherichia coli are, unusually, nearly all short deletions, perhaps caused by slipped-strand mispairings in mononucleotide runs. But are they directed?

Journal: :Journal of Alzheimer's Disease 2021

Background: The most common cause of early-onset familial Alzheimer’s disease (EOfAD) is mutations in PRESENILIN 1 (PSEN1) allowing production mRNAs encoding full-length, but mutant, proteins. In contrast, a single known frameshift mutation PSEN1 causes acne inversa (fAI) without EOfAD. molecular consequences heterozygosity for these types, and how they completely different diseases, remains la...

Journal: :Gastroenterology 2016
Ling-Shiang Chuang Nicole Villaverde Ken Y Hui Arthur Mortha Adeeb Rahman Adam P Levine Talin Haritunians Sok Meng Evelyn Ng Wei Zhang Nai-Yun Hsu Jody-Ann Facey Tramy Luong Heriberto Fernandez-Hernandez Dalin Li Manuel Rivas Elena R Schiff Alexander Gusev L Phillip Schumm Beatrice M Bowen Yashoda Sharma Kaida Ning Romain Remark Sacha Gnjatic Peter Legnani James George Bruce E Sands Joanne M Stempak Lisa W Datta Seth Lipka Seymour Katz Adam S Cheifetz Nir Barzilai Nikolas Pontikos Clara Abraham Marla J Dubinsky Stephan Targan Kent Taylor Jerome I Rotter Ellen J Scherl Robert J Desnick Maria T Abreu Hongyu Zhao Gil Atzmon Itsik Pe'er Subra Kugathasan Hakon Hakonarson Jacob L McCauley Todd Lencz Ariel Darvasi Vincent Plagnol Mark S Silverberg Aleixo M Muise Steven R Brant Mark J Daly Anthony W Segal Richard H Duerr Miriam Merad Dermot P B McGovern Inga Peter Judy H Cho

BACKGROUND & AIMS Crohn's disease (CD) has the highest prevalence in Ashkenazi Jewish populations. We sought to identify rare, CD-associated frameshift variants of high functional and statistical effects. METHODS We performed exome sequencing and array-based genotype analyses of 1477 Ashkenazi Jewish individuals with CD and 2614 Ashkenazi Jewish individuals without CD (controls). To validate ...

2017
Xue-Yan Qin Pei-Zeng Jia Hua-Xiang Zhao Wei-Ran Li Feng Chen Jiu-Xiang Lin

BACKGROUND Cleidocranial dysplasia (CCD) is an autosomal dominant disease that affects the skeletal system. Common symptoms of CCD include hypoplasia or aplasia of the clavicles, delayed or even absent closure of the fontanels, midface hypoplasia, short stature, and delayed eruption of permanent and supernumerary teeth. Previous studies reported a connection between CCD and the haploinsufficien...

Journal: :Genetics 2004
Mary-Jane Lombardo Ildiko Aponyi Susan M Rosenberg

Microbial cells under growth-limiting stress can generate mutations by mechanisms distinct from those in rapidly growing cells. These mechanisms might be specific stress responses that increase mutation rates, potentially altering rates of evolution, or might reflect non-stress-specific processes in rare growing cells. In an Escherichia coli model system, both frameshift reversion mutations and...

Journal: :Neurobiology of aging 2015
Kelly L Williams Emily P McCann Jennifer A Fifita Katharine Zhang Emma L Duncan Paul J Leo Mhairi Marshall Dominic B Rowe Garth A Nicholson Ian P Blair

Missense and frameshift mutations in TRAF family member-associated NF-kappa-B activator (TANK)-binding kinase 1 (TBK1) have been reported in European sporadic and familial amyotrophic lateral sclerosis (ALS) cohorts. To assess the role of TBK1 in ALS patient cohorts of wider ancestry, we have analyzed whole-exome sequence data from an Australian cohort of familial ALS (FALS) patients and contro...

2016
Xiao-Jun Chen Hong Zhang Zhi-Ping Tan Wen Hu Yi-Feng Yang

Multiple osteochondromas (MO), also known as hereditary multiple exostoses, is an autosomal dominant bone disorder. Mutations in exostosin glycosyl transferase‑1 (EXT1) and exostosin glycosyl transferase‑2 (EXT2), including missense, nonsense, frameshift and splice‑site mutations, account for up to 80% of reported cases. The proteins EXT1 and EXT2 form a hetero‑oligomeric complex that functions...

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