According to the American Thoracic Society (ATS)/European Respiratory Society consensus classification, idiopathic interstitial pneumonias (IIPs) include several clinic-radiologic-pathologic entities: idiopathic pulmonary fibrosis (IPF), usual interstitial pneumonia (UIP), nonspecific interstitial pneumonia (NSIP), cryptogenic organizing pneumonia, acute interstitial pneumonia, respiratory bron...

Idiopathic pulmonary fibrosis (IPF) is the most common and fatal idiopathic interstitial pneumonia characterized by chronic progressive of indeterminate etiology. In 2018, American Thoracic Society, European Respiratory Japanese Latin Society published joint clinical practice guidelines for IPF. The require exclusion known causes lung disease identification a radiological and/or pathologic patt...