Malignant peripheral nerve sheath tumor (MPNST) is an aggressive neoplasm of neural origin. It is a rare neoplasm of childhood, accounting for less than 5% of all cases. In 1994 a 29 months old boy was admitted to the Mofid Hospital with complaints of fever, dyspnea and respiratory distress. After performing all the necessary clinical and labratory tests a large mass in the upper posterior medi...