The congenital aplasia or severe hypoplasia of mullerian structures is infrequent. However, the features of normal female endocrine function paired with the absence of a functional uterus and vagina makes it a fascinating entity. The diagnosis and work-up in these patients has become very efficient, thanks to the use of imaging, and there are multiple successful procedures for the creation of a...

Herlyn-Werner-Wunderlich syndrome (HWWS), characterized by uterus didelphys, obstructed hemivagina, and associated with ipsilateral renal agenesis, is an uncommon combined Mullerian and mesonephric duct anomaly. We are reporting a case of 12 year old Female presented with lower abdominal pain, clinically as suspected to have lower abdominal mass. On subsequent radiological investigation patient...

Mayer-Rokitansky-Kuster-Hauser (MRKH) syndrome is characterized by Mullerian duct aplasia in an XX individual with female phenotype presenting primary amenorrhea at adolescence. Multiple abnormalities may be associated with the MRKH syndrome. Genetic investigations focused on the genes of anti-Mullerian hormone and its receptor, as well as on Wt1, Pax2, Cftr and Hox genes, have been unproductiv...

Background: The Vagina is a composite structure formed partly from the mullerian duct and partly from urogential sinus. Most of the patients with mullerian agenesis have small rudimentary uterus without any endometrial cavity, 7% 8% may have functioning uterus. Case: A 15 years old girl admitted with primary amenorrhea, cyclical abdominal pain, hematometra and complete vaginal agenesis. Surgica...

Bicornuate and septate uteri are among the commonest Mullerian anomalies. They are sporadic and fairly distinguished, but hybrid deformities can occur. This combination creates aetiological and clinical difficulties. The alternative theory of concurrent fusion and septal resorption of the Mullerian duct is seen as the basis of the altered foetal embryology, while the favourable outlook of a bic...

Herlyn-Werner-Wunderlich (HWW) syndrome is a rare variant of mullerian duct anomalies characterized by the triad uterine didelphys, obstructed hemivagina and ipsilateral renal agenesis. We report two cases HWW in young women with abdominal pain. This diagnosis can easily be missed if clinician not aware syndrome. In one case, computed tomography image hematocolpos was initially mistaken for cys...

CONTEXT Pancreas divisum is a congenital anomaly in which the ventral and dorsal pancreatic ducts do not communicate. CASE REPORT Autopsy case of pancreas divisum with a history of heavy consumption of alcohol was presented. Pancreatography via the major duodenal papilla showed a short ventral pancreatic duct of 1 cm in length, and hypoplasia of the ventral pancreas was suspected. As large cy...

Unicornuate uterus is a rare congenital anomaly which occurs due to partial development of mullerian duct system. Patient with unicornuate uterus usually present with dysmenorrhoea, hematometra and endometriosis during their reproductive period. In the absence of these symptoms, proper identification and diagnosis of mullerian anomaly becomes difficult. Sometimes during laparoscopy it can mimic...

Study sample No sample size appears to have been determined in the planning phase of the study. In addition, no retrospective power calculations were reported. The authors reported that a group of MIS-TKA patients was compared with a group of 50 traditional TKA patients, but it was unclear how many patients were in the MIS-TKA group. The authors then reported that all patients (n=159) were coho...