نتایج جستجو برای: netherton syndrome

تعداد نتایج: 621922  

Journal: :Acta dermato-venereologica 2015
Liliana Guerra Paola Fortugno Cristina Pedicelli Cinzia Mazzanti Vittoria Proto Giovanna Zambruno Daniele Castiglia

Ichthyosis linearis circumflexa (ILC) presents as serpiginous and migratory erythematous patches with double-edged scales. ILC is rarely an isolated skin manifestation, but most commonly a part of Netherton syndrome (NS). NS is caused by SPINK5 mutations, which lead to absent or sometimes reduced expression of the serine protease inhibitor LEKTI. NS is characterised by congenital ichthyosiform ...

Journal: :The international journal of biochemistry & cell biology 2002
Hans Jürgen Mägert Peter Kreutzmann Ludger Ständker Michael Walden Katrin Drögemüller Wolf Georg Forssmann

Proteinase inhibitors are important negative regulators of proteinase action in vivo and are thus involved in several pathophysiological processes. Starting with the isolation of two new peptides from human blood filtrate, we succeeded in cloning a cDNA encoding the precursor protein for a novel 15-domain Kazal-type-related serine proteinase inhibitor. Two of the 15 domains almost exactly match...

نمودار تعداد نتایج جستجو در هر سال

با کلیک روی نمودار نتایج را به سال انتشار فیلتر کنید