نتایج جستجو برای: pfapa
تعداد نتایج: 261 فیلتر نتایج به سال:
Methods The study group consisted of 339 FMF patients diagnosed according to Tel Hashomer criteria. A control group of 377 patients were diagnosed other periodic fever syndromes including MKD, TRAPS, CAPS and PFAPA syndromes. Both groups were evaluated according to the Tel Hashomer criteria and the new set of diagnostic criteria proposed to use in childhood FMF. The diagnostic performance of bo...
The Periodic Fever, Aphthous stomatitis, Pharyngitis and cervical Adenitis (PFAPA) syndrome is the most common of the autoinflammatory syndromes in childhood. Symptoms may highly mimic recurrent tonsillitis, and tonsillectomy may be an option for cure in these patients. It is therefore of high interest for otolaryngologists to be aware of and updated on this syndrome, to avoid overlooking the s...
Methods We conducted a retrospective study on patients with clinical diagnosis of PFAPA syndrome followed at a tertiary center from January 1993 to August 2010. Clinical and laboratory parameters have been evaluated at onset and during the follow-up. Disease remission was considered as the absence of symptoms for at least one year. Disease outcome in patients who underwent tonsillectomy was com...
Methods A web-based registry collecting baseline and clinical information of autoinflammatory diseases was located at the member area of the PRINTO website (www.printo. it). Participating hospitals included pediatric rheumatology centers of the PRINTO network and adult centers with a specific interest in autoinflammatory diseases. Data was collected on Blau’s syndrome, Behçet’s disease, CAPS, C...
Introduction PFAPA is a pediatric auto-inflammatory syndrome of unknown etiology, characterized by recurrent fever, aphthosis, pharyngitis and cervical adenitis. Dysregulated monocyte interleukin-1 beta (IL-1b) secretion is thought to play an important role in fever flares. Recently, it was published that Thp1 cells (a monocytic cell line) transduced with the Q705K variant of NLRP3 increased IL...
Anti-IL1ß-monoclonal antibody in two adult patients with PFAPA Syndrome - a single centre experience
Background The periodic fever, aphthous stomatitis, pharyngitis and cervical adenitis (PFAPA) syndrome belongs to the rare nonhereditary autoinflammatory diseases and normally onsetting in childhood, but despite of tonsillectomy persisting or newly occurring in adulthood. The exact pathogenesis is not clear, but to our understanding it is an acquired autoinflammatory disease due to an unregulat...
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