Agenesis of the inferior vena cava (IVC) is a rare anomaly which can be identified as incidental finding or can be associated with iliofemoral vein thrombosis. IVC agenesis has a known association with renal anomalies which are mainly confined to the right kidney. We describe a case of a 14-year-old male who presented with left leg swelling and pain. Ultrasonography confirmed the presence of le...

Obstructed hemi-vagina and ipsilateral renal agenesis (OHVIRA) syndrome is a complex of Müllerian Wolffian duct anomalies constituted by obstructed that may form hematocolpos with anomaly different degrees didelphic uterine anomalies. Due to the obstructive reproductive tract, endometriosis differing severities be common complication OHVIRA syndrome. Here, we report three women showed clinical ...

We aimed to discuss the prenatal diagnosis and pathological features of sirenomelia, and to review current embryogenic theories. We observed two sirenomelic fetuses that were at the 19th and 16th gestational week respectively. In the former, transvaginal ultrasound revealed severe oligohydramnios and internal abortion, whereas bilateral renal agenesis, absence of a normally tapered lumbosacral ...

A rare case of seminal vesicle cyst associated with ipsilateral renal agenesis is reported. The role of ultrasonography and computed tomography in diagnosis and management is discussed. Congenital malformations of the seminal vesicle are most uncommon and most of them are cystic malformation. Approximately two thirds of them are associated with ipsilateral renal agenesis, since both the uretera...

Branchio-oto-renal syndrome (Melnick-Fraser syndrome) is a rare autosomal dominant disorder characterized by syndromic association of branchial cysts or fistulae along with external, middle & inner ear malformations and renal anomalies. Authors are reporting a 19 year male patient, who presented with profound deafness & low set "lop-ear" with right sided preauricular pit. USG abdomen revealed a...

Herlyn-Werner-Wunderlich (HWW) syndrome is an uncommon combined müllerian duct anomalies (MDAs) and mesonephric duct malformation of female urogenital tract characterized by uterus didelphys and obstructed hemi-vagina and ipsilateral renal agenesis (OHVIRA) syndrome. We present a rare and unusual case of this syndrome in a 19 year-old female who suffered from hypomenorrhoea and abdominal pain. ...

UNLABELLED To help physicians and radiologists in the diagnosis of female genito-urinary malformations, especially of complex cases, the embryology of the female genital tract, the basis for Müllerian development anomalies, the current classifications for such anomalies and the comparison for inclusion and cataloguing of female genital malformations are briefly reviewed. The use of the embryolo...

Herlyn-Werner-Wunderlich (HWW) syndrome is a rare variant of mullerian duct anomalies characterized by the triad uterine didelphys, obstructed hemivagina and ipsilateral renal agenesis. We report two cases HWW in young women with abdominal pain. This diagnosis can easily be missed if clinician not aware syndrome. In one case, computed tomography image hematocolpos was initially mistaken for cys...

There are many reasons for solitary kidney. Congenital causes include renal agenesis and dysplasia. Acquired nephrectomy performed including traumatic kidney injury, disease (e.g., cell carcinoma), donation transplantation. According to the European Association of Urology, World Society Emergency Surgery, American Surgery Trauma guidelines, it is important preserve remaining function as much po...