نتایج جستجو برای: seipin

تعداد نتایج: 156  

2016
Mohammad Reza Alaei Saeed Talebi Mohammad Ghofrani Mohsen Taghizadeh Mohammad Keramatipour

BACKGROUND Progressive encephalopathy with or without lipodystrophy is a rare autosomal recessive childhood-onset seipin-associated neurodegenerative syndrome, leading to developmental regression of motor and cognitive skills. In this study, we introduce a patient with developmental regression and autism. The causative mutation was found by exome sequencing. METHODS The proband showed a gener...

2018
Michal Eisenberg-Bord Muriel Mari Uri Weill Eden Rosenfeld-Gur Ofer Moldavski Inês G Castro Krishnakant G Soni Nofar Harpaz Tim P Levine Anthony H Futerman Fulvio Reggiori Vytas A Bankaitis Maya Schuldiner Maria Bohnert

Functional heterogeneity within the lipid droplet (LD) pool of a single cell has been observed, yet the underlying mechanisms remain enigmatic. Here, we report on identification of a specialized LD subpopulation characterized by a unique proteome and a defined geographical location at the nucleus-vacuole junction contact site. In search for factors determining identity of these LDs, we screened...

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